Titre : Hypertension artérielle pulmonaire primitive familiale

Hypertension artérielle pulmonaire primitive familiale : Questions médicales fréquentes

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confirmer le diagnostic ?\nQuels symptômes peuvent alerter sur cette maladie ?\nL'hérédité joue-t-elle un rôle dans le diagnostic ?\nQuels examens complémentaires sont recommandés ?", "url": "https://questionsmedicales.fr/mesh/D065627?page=2#section-diagnostic" }, { "@type": "MedicalWebPage", "name": "Symptômes", "headline": "Symptômes sur Hypertension artérielle pulmonaire primitive familiale", "description": "Quels sont les symptômes principaux de cette maladie ?\nLes symptômes varient-ils selon les patients ?\nQuand les symptômes apparaissent-ils généralement ?\nLes symptômes peuvent-ils s'aggraver avec le temps ?\nY a-t-il des signes d'alerte à surveiller ?", "url": "https://questionsmedicales.fr/mesh/D065627?page=2#section-symptômes" }, { "@type": "MedicalWebPage", "name": "Prévention", "headline": "Prévention sur Hypertension artérielle pulmonaire primitive familiale", "description": "Peut-on prévenir l'hypertension pulmonaire ?\nLes facteurs de risque peuvent-ils être modifiés ?\nLe dépistage précoce est-il important ?\nLes activités physiques sont-elles recommandées ?\nY a-t-il des conseils diététiques à suivre ?", "url": "https://questionsmedicales.fr/mesh/D065627?page=2#section-prévention" }, { "@type": "MedicalWebPage", "name": "Traitements", "headline": "Traitements sur Hypertension artérielle pulmonaire primitive familiale", "description": "Quels traitements sont disponibles pour cette maladie ?\nLa transplantation pulmonaire est-elle une option ?\nLes médicaments peuvent-ils améliorer la qualité de vie ?\nY a-t-il des effets secondaires aux traitements ?\nLes traitements sont-ils personnalisés ?", "url": "https://questionsmedicales.fr/mesh/D065627?page=2#section-traitements" }, { "@type": "MedicalWebPage", "name": "Complications", "headline": "Complications sur Hypertension artérielle pulmonaire primitive familiale", "description": "Quelles sont les complications possibles ?\nL'hypertension pulmonaire peut-elle affecter d'autres organes ?\nComment l'insuffisance cardiaque est-elle liée ?\nLes complications peuvent-elles être évitées ?\nQuels signes indiquent une complication ?", "url": "https://questionsmedicales.fr/mesh/D065627?page=2#section-complications" }, { "@type": "MedicalWebPage", "name": "Facteurs de risque", "headline": "Facteurs de risque sur Hypertension artérielle pulmonaire primitive familiale", "description": "Quels sont les principaux facteurs de risque ?\nL'âge influence-t-il le risque ?\nLes maladies auto-immunes sont-elles un facteur ?\nLe sexe joue-t-il un rôle dans le risque ?\nLe mode de vie peut-il influencer le risque ?", "url": "https://questionsmedicales.fr/mesh/D065627?page=2#section-facteurs de risque" } ] }, { "@type": "FAQPage", "mainEntity": [ { "@type": "Question", "name": "Comment diagnostiquer l'hypertension pulmonaire ?", "position": 1, "acceptedAnswer": { "@type": "Answer", "text": "Le diagnostic se fait par échocardiographie, tests de fonction pulmonaire et cathétérisme cardiaque." } }, { "@type": "Question", "name": "Quels tests sont utilisés pour confirmer le diagnostic ?", "position": 2, "acceptedAnswer": { "@type": "Answer", "text": "Le cathétérisme cardiaque droit est le test de référence pour mesurer la pression pulmonaire." } }, { "@type": "Question", "name": "Quels symptômes peuvent alerter sur cette maladie ?", "position": 3, "acceptedAnswer": { "@type": "Answer", "text": "Essoufflement, fatigue, douleurs thoraciques et syncope sont des symptômes courants." } }, { "@type": "Question", "name": "L'hérédité joue-t-elle un rôle dans le diagnostic ?", "position": 4, "acceptedAnswer": { "@type": "Answer", "text": "Oui, un historique familial d'hypertension pulmonaire augmente le risque de la maladie." } }, { "@type": "Question", "name": "Quels examens complémentaires sont recommandés ?", "position": 5, "acceptedAnswer": { "@type": "Answer", "text": "Des tests génétiques peuvent être effectués pour identifier des mutations associées." } }, { "@type": "Question", "name": "Quels sont les symptômes principaux de cette maladie ?", "position": 6, "acceptedAnswer": { "@type": "Answer", "text": "Les symptômes incluent essoufflement, fatigue, douleurs thoraciques et palpitations." } }, { "@type": "Question", "name": "Les symptômes varient-ils selon les patients ?", "position": 7, "acceptedAnswer": { "@type": "Answer", "text": "Oui, l'intensité et la combinaison des symptômes peuvent varier d'un patient à l'autre." } }, { "@type": "Question", "name": "Quand les symptômes apparaissent-ils généralement ?", "position": 8, "acceptedAnswer": { "@type": "Answer", "text": "Les symptômes peuvent apparaître progressivement, souvent après l'adolescence ou à l'âge adulte." } }, { "@type": "Question", "name": "Les symptômes peuvent-ils s'aggraver avec le temps ?", "position": 9, "acceptedAnswer": { "@type": "Answer", "text": "Oui, sans traitement, les symptômes peuvent s'aggraver et affecter la qualité de vie." } }, { "@type": "Question", "name": "Y a-t-il des signes d'alerte à surveiller ?", "position": 10, "acceptedAnswer": { "@type": "Answer", "text": "Des signes comme l'œdème des jambes ou des lèvres bleues doivent être surveillés." } }, { "@type": "Question", "name": "Peut-on prévenir l'hypertension pulmonaire ?", "position": 11, "acceptedAnswer": { "@type": "Answer", "text": "Il n'existe pas de méthode de prévention spécifique, mais un suivi médical régulier est conseillé." } }, { "@type": "Question", "name": "Les facteurs de risque peuvent-ils être modifiés ?", "position": 12, "acceptedAnswer": { "@type": "Answer", "text": "Oui, éviter le tabagisme et maintenir un poids santé peut réduire le risque." } }, { "@type": "Question", "name": "Le dépistage précoce est-il important ?", "position": 13, "acceptedAnswer": { "@type": "Answer", "text": "Oui, un dépistage précoce peut aider à identifier la maladie avant qu'elle ne progresse." } }, { "@type": "Question", "name": "Les activités physiques sont-elles recommandées ?", "position": 14, "acceptedAnswer": { "@type": "Answer", "text": "Des exercices modérés peuvent être bénéfiques, mais doivent être adaptés à chaque patient." } }, { "@type": "Question", "name": "Y a-t-il des conseils diététiques à suivre ?", "position": 15, "acceptedAnswer": { "@type": "Answer", "text": "Une alimentation équilibrée et faible en sel peut aider à gérer la pression artérielle." } }, { "@type": "Question", "name": "Quels traitements sont disponibles pour cette maladie ?", "position": 16, "acceptedAnswer": { "@type": "Answer", "text": "Les traitements incluent des vasodilatateurs, des anticoagulants et des thérapies ciblées." } }, { "@type": "Question", "name": "La transplantation pulmonaire est-elle une option ?", "position": 17, "acceptedAnswer": { "@type": "Answer", "text": "Oui, la transplantation pulmonaire peut être envisagée pour les cas graves et réfractaires." } }, { "@type": "Question", "name": "Les médicaments peuvent-ils améliorer la qualité de vie ?", "position": 18, "acceptedAnswer": { "@type": "Answer", "text": "Oui, les traitements peuvent soulager les symptômes et améliorer la qualité de vie des patients." } }, { "@type": "Question", "name": "Y a-t-il des effets secondaires aux traitements ?", "position": 19, "acceptedAnswer": { "@type": "Answer", "text": "Oui, certains traitements peuvent avoir des effets secondaires comme des maux de tête ou des nausées." } }, { "@type": "Question", "name": "Les traitements sont-ils personnalisés ?", "position": 20, "acceptedAnswer": { "@type": "Answer", "text": "Oui, le traitement est souvent adapté en fonction de la gravité et des caractéristiques du patient." } }, { "@type": "Question", "name": "Quelles sont les complications possibles ?", "position": 21, "acceptedAnswer": { "@type": "Answer", "text": "Les complications incluent l'insuffisance cardiaque, les arythmies et les embolies pulmonaires." } }, { "@type": "Question", "name": "L'hypertension pulmonaire peut-elle affecter d'autres organes ?", "position": 22, "acceptedAnswer": { "@type": "Answer", "text": "Oui, elle peut entraîner des complications dans le cœur, les reins et le foie." } }, { "@type": "Question", "name": "Comment l'insuffisance cardiaque est-elle liée ?", "position": 23, "acceptedAnswer": { "@type": "Answer", "text": "L'augmentation de la pression dans les artères pulmonaires peut surcharger le cœur, entraînant une insuffisance." } }, { "@type": "Question", "name": "Les complications peuvent-elles être évitées ?", "position": 24, "acceptedAnswer": { "@type": "Answer", "text": "Un traitement précoce et un suivi régulier peuvent aider à prévenir certaines complications." } }, { "@type": "Question", "name": "Quels signes indiquent une complication ?", "position": 25, "acceptedAnswer": { "@type": "Answer", "text": "Des symptômes comme une aggravation de l'essoufflement ou des douleurs thoraciques doivent alerter." } }, { "@type": "Question", "name": "Quels sont les principaux facteurs de risque ?", "position": 26, "acceptedAnswer": { "@type": "Answer", "text": "Les antécédents familiaux, certaines maladies et le tabagisme sont des facteurs de risque connus." } }, { "@type": "Question", "name": "L'âge influence-t-il le risque ?", "position": 27, "acceptedAnswer": { "@type": "Answer", "text": "Oui, le risque augmente généralement avec l'âge, surtout après 30 ans." } }, { "@type": "Question", "name": "Les maladies auto-immunes sont-elles un facteur ?", "position": 28, "acceptedAnswer": { "@type": "Answer", "text": "Oui, des maladies comme le lupus ou la sclérodermie peuvent augmenter le risque d'hypertension pulmonaire." } }, { "@type": "Question", "name": "Le sexe joue-t-il un rôle dans le risque ?", "position": 29, "acceptedAnswer": { "@type": "Answer", "text": "Oui, les femmes sont plus souvent touchées par l'hypertension pulmonaire que les hommes." } }, { "@type": "Question", "name": "Le mode de vie peut-il influencer le risque ?", "position": 30, "acceptedAnswer": { "@type": "Answer", "text": "Oui, un mode de vie sédentaire et une mauvaise alimentation peuvent augmenter le risque." } } ] } ] }

Sources (10000 au total)

Methamphetamine-associated pulmonary arterial hypertension.

Methamphetamine use is increasing in popularity globally, and chronic users suffer from various drug toxicities, including the development of pulmonary arterial hypertension. Although it was previousl... The mechanism by which methamphetamine abuse leads to pulmonary hypertension is unclear. However, recent studies have suggested that reduced expression of carboxylesterase 1 may be implicated due to m... Future studies are needed to better understand the mechanism by which methamphetamine use leads to pulmonary arterial hypertension. Methamphetamine-associated pulmonary arterial hypertension likely re...

Right ventricular assessment in pulmonary hypertension.

The purpose of this review is to provide an overview of assessment of right ventricular function in the context of pulmonary hypertension and pulmonary arterial hypertension (PAH). We will review uniq... The importance of performance in prognosis and risk assessment in patients with pulmonary hypertension has been continually emphasized in ongoing research. Representative parameters of right ventricul... Careful evaluation of right ventricular function is paramount in assessing the cause of pulmonary hypertension and severity of disease. Further, it has prognostic significance, as many representative ...

CTLA-4 Expression Is a Promising Biomarker of Idiopathic Pulmonary Arterial Hypertension and Allows Differentiation of the Type of Pulmonary Hypertension.

Pulmonary arterial hypertension (PAH) is an increasingly frequently diagnosed disease, the molecular mechanisms of which have not been thoroughly investigated. The aim of our study was to investigate ...

Anticoagulation in pulmonary arterial hypertension - association with mortality, healthcare utilization, and quality of life: The Pulmonary Hypertension Association Registry (PHAR).

Routine long-term anticoagulation in pulmonary arterial hypertension (PAH) is controversial. To date, anticoagulation has been found to be beneficial or neutral in idiopathic disease (IPAH) and neutra... The PHAR is a prospective registry of PAH patients referred to 58 pulmonary hypertension care centers in the United States. We compared patients who received anticoagulation during enrollment (questio... Anticoagulation is not associated with higher mortality, but is associated with increased healthcare utilization in the PHAR. PAH-specific QoL may be worse in patients receiving anticoagulation. The r...

Diversity of hemodynamic types in connective tissue disease associated pulmonary hypertension: more than a subgroup of pulmonary arterial hypertension.

Connective tissue disease associated pulmonary hypertension (CTD-PH) is classified as a subgroup of WHO group 1 PH, also called pulmonary arterial hypertension (PAH). However, not all CTD-PH fit hemod... We performed a retrospective cohort study. CTD-PH patients were enrolled and divided into WHO group1 PH, WHO group 2 PH and hyperdynamic PH (mPAP > 20 mmHg, PVR < 3WU, PAWP < 15 mmHg) according to hem... A total of 202 CTD-PH patients were included, 138 in WHO group 1 PH, 33 in WHO group 2 PH and 31 in hyperdynamic PH. We found hyperdynamic PH is less severe, presenting lower NT-proBNP level, better W... Considering diversity in hemodynamic types, CTD-PH is more than a subgroup of PAH. Different types of CTD-PH present different clinical phenotypes and outcome. Phenotyping PH in CTD-PH patients is imp...

Approach to the hospitalized patient with pulmonary arterial hypertension.

Hospitalization in pulmonary arterial hypertension (PAH) patients is an important clinical worsening event significantly associated with subsequent mortality. Furthermore, irrespective of the cause of... This article covers recent literature describing risk factors, predictors of outcome and state-of the art management approach to a hospitalized PAH patients with a special focus on management of RV fa... The review highlights the importance of multidisciplinary approach to a hospitalized PAH patient and highlight important implications in clinical practice and knowledge gaps for potential future resea...

Role of the electrocardiogram in the risk stratification of pulmonary hypertension.

The prognosis of pulmonary arterial hypertension (PAH) and chronic thromboembolic pulmonary hypertension (CTEPH) remains dismal. Better risk prediction is needed. This study investigated the prognosti... In this single-centre prospective study, consecutive treatment-naïve patients with PAH or CTEPH were included at time of diagnosis. From the 12-lead ECG, obtained at baseline, the following parameters... In total, 140 patients were included (median age: 60.7 years, 63.6% female). The ECG was abnormal in 86.2%: sinus rhythm was not present in 9.3%, right QRS axis was observed in 47.8%, mean QRS duratio... Only 13.8% of patients with PAH and CTEPH presented with a normal ECG, which is associated with favourable outcome. The ECG provides additional prognostic value to current clinical parameters and shou...