Pityriasis Rubra Pilaris With Extensive Follicular Acantholysis Resembling Pemphigus Vulgaris: A Case Report.
Journal
The American Journal of dermatopathology
ISSN: 1533-0311
Titre abrégé: Am J Dermatopathol
Pays: United States
ID NLM: 7911005
Informations de publication
Date de publication:
Jan 2019
Jan 2019
Historique:
pubmed:
26
7
2018
medline:
23
4
2019
entrez:
26
7
2018
Statut:
ppublish
Résumé
Pityriasis rubra pilaris (PRP) is a rare, chronic, heterogeneous, papulosquamous inflammatory dermatosis of unknown etiology. Although erythematous scaly patches characterize the classic presentation of PRP, a broad range of clinical presentations has been reported. Histologically, PRP is characterized by psoriasiform acanthosis with alternating orthokeratosis and parakeratosis and rarely small acantholytic foci. In this article, we report a patient who presented with diffuse erythroderma and extensive acantholysis mimicking pemphigus vulgaris histologically.
Identifiants
pubmed: 30045068
doi: 10.1097/DAD.0000000000001222
doi:
Substances chimiques
Immunosuppressive Agents
0
Steroids
0
Types de publication
Case Reports
Journal Article
Langues
eng
Sous-ensembles de citation
IM