Phase 3 study of recombinant von Willebrand factor in patients with severe von Willebrand disease who are undergoing elective surgery.


Journal

Journal of thrombosis and haemostasis : JTH
ISSN: 1538-7836
Titre abrégé: J Thromb Haemost
Pays: England
ID NLM: 101170508

Informations de publication

Date de publication:
01 2019
Historique:
received: 24 04 2018
pubmed: 27 10 2018
medline: 14 4 2020
entrez: 27 10 2018
Statut: ppublish

Résumé

Essentials Recombinant von Willebrand factor (rVWF) is effective in von Willebrand disease (VWD). A phase 3 study of rVWF, with/without recombinant factor VIII (rFVIII) before surgery in VWD. Overall rVWF's efficacy was rated excellent/good; rVWF was administered alone in most patients. rVWF was well-tolerated and hemostasis was achieved in patients with severe VWD undergoing surgery. SUMMARY: Background Recombinant von Willebrand factor (rVWF) has demonstrated efficacy for on-demand treatment of bleeding in severe von Willebrand disease (VWD), warranting evaluation in the surgical setting. Objectives This study (NCT02283268) evaluated the hemostatic efficacy/safety profile of rVWF, with/without recombinant factor VIII (rFVIII), in patients with severe VWD undergoing surgery. Patients/Methods Patients received rVWF 40-60 IU kg

Identifiants

pubmed: 30362288
doi: 10.1111/jth.14313
pmc: PMC7379610
pii: S1538-7836(22)03020-3
doi:

Substances chimiques

Coagulants 0
Recombinant Proteins 0
von Willebrand Factor 0

Types de publication

Clinical Trial, Phase III Journal Article Multicenter Study Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

52-62

Subventions

Organisme : Baxalta
Pays : International

Commentaires et corrections

Type : CommentIn
Type : CommentIn

Informations de copyright

© 2018 Shire International GmbH Journal of Thrombosis and Haemostasis © 2018 International Society on Thrombosis and Haemostasis.

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Auteurs

F Peyvandi (F)

Fondazione IRCCS Ca' Granda Ospedale Maggiore Policlinico, Angelo Bianchi Bonomi Hemophilia and Thrombosis Center, Milan, Italy.
Department of Pathophysiology and Transplantation, University of Milan, Milan, Italy.

A Mamaev (A)

Regional State Budgetary Healthcare Institution "Regional Clinical Hospital", Barnaul, Altai Region, Russian Federation.

J-D Wang (JD)

Center for Rare Diseases and Hemophilia Center, Taichung Veterans General Hospital, Taichung, Taiwan.

O Stasyshyn (O)

SI Institute of Blood Pathology and Transfusion Medicine of NAMS of Ukraine, Lviv, Ukraine.

M Timofeeva (M)

Federal State Budgetary Research Institution "Kirov Scientific and Research Institute of Hematology and Blood Transfusion of Federal Medico-Biological Agency of Russia", Kirov, Russian Federation.

N Curry (N)

The Oxford Haemophilia and Thrombosis Centre, Churchill Hospital and NIHR BRC, Blood Theme, Oxford, UK.

A R Cid (AR)

Hospital Universitario y Politécnico La Fe Hemostasia y Trombosis, Valencia, Spain.

T T Yee (TT)

Royal Free London NHS Foundation Trust, Katharine Dormandy Haemophilia and Thrombosis Centre, London, UK.

K Kavakli (K)

Ege Universitesi Tip Fakultesi Hematoloji Bilim Dali, Bornova, Izmir, Turkey.

G Castaman (G)

Center for Bleeding Disorders and Coagulation, Department of Oncology, Careggi University Hospital, Florence, Italy.

A Sytkowski (A)

Shire, Cambridge, MA, USA.

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Classifications MeSH