Phosphomimetic-mediated in vitro rescue of hypertrophic cardiomyopathy linked to R58Q mutation in myosin regulatory light chain.
R58Q mutation
S15D-phosphorylation mimic
muscle contraction
myosin regulatory light chain
rescue of function
super-relaxed state
Journal
The FEBS journal
ISSN: 1742-4658
Titre abrégé: FEBS J
Pays: England
ID NLM: 101229646
Informations de publication
Date de publication:
01 2019
01 2019
Historique:
received:
05
07
2018
revised:
03
10
2018
accepted:
13
11
2018
pubmed:
16
11
2018
medline:
10
7
2019
entrez:
16
11
2018
Statut:
ppublish
Résumé
Myosin regulatory light chain (RLC) phosphorylation is important for cardiac muscle mechanics/function as well as for the Ca
Identifiants
pubmed: 30430732
doi: 10.1111/febs.14702
pmc: PMC6326841
mid: NIHMS997858
doi:
Substances chimiques
Actins
0
Myosin Light Chains
0
Calcium
SY7Q814VUP
Banques de données
PDB
['3jvtB', '2w4aA', '1prwA', '2mysB', '4mvfA', '4agrA', '4ik1A']
Types de publication
Journal Article
Research Support, N.I.H., Extramural
Research Support, Non-U.S. Gov't
Langues
eng
Sous-ensembles de citation
IM
Pagination
151-168Subventions
Organisme : NHLBI NIH HHS
ID : R01 HL071778
Pays : United States
Organisme : NHLBI NIH HHS
ID : R01 HL123255
Pays : United States
Organisme : NIH HHS
ID : HL123255
Pays : United States
Organisme : American Heart Association
ID : 17PRE33650085
Pays : International
Informations de copyright
© 2018 Federation of European Biochemical Societies.
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