mTOR inhibitors in pediatric liver transplant recipients.


Journal

Clinics and research in hepatology and gastroenterology
ISSN: 2210-741X
Titre abrégé: Clin Res Hepatol Gastroenterol
Pays: France
ID NLM: 101553659

Informations de publication

Date de publication:
08 2019
Historique:
received: 27 06 2018
revised: 05 11 2018
accepted: 09 11 2018
pubmed: 12 12 2018
medline: 7 7 2020
entrez: 12 12 2018
Statut: ppublish

Résumé

During the past decade, mTOR inhibitors (mTORi), everolimus and sirolimus, have been increasingly used after adult liver transplantation (LT). The aim of the present study was to describe the use of mTORi in pediatric LT recipients. All pediatric LT recipients who received mTORi before December 2017 from 4 European pediatric LT centers were included and analyzed. The present retrospective study included 30 patients; 21 were male (70%), median age was 9.3 years (range: 1.2-17.1 years) at mTORi introduction. Main indications for mTORi introduction were pre-existing liver malignancy (43.3%), calcineurin inhibitor (CNI) nephrotoxicity (26.7%), or rejection (23.4%). At last follow-up, mTORi CNIs were withdrawn in 10 patients (10/29, 34.5%). The median dose of mTORi was 1.8 mg/day (range: 0.3-5.0) or 0.058 mg/kg/day (range: 0.01-0.26), and the median trough level was 5.1 μg/L (range: 1.0-15.5). After a median follow-up of 2.8 years (range: 0.2-10.0), 50.0% of the patients presented with at least one adverse event. The main adverse events included hyperlipidemia, proteinuria, dermatitis, and mucitis. Overall mTORi discontinuation rate was 23.3% (10.0% because of adverse event). Introduction of mTORi had no significant impact on renal function. Our results suggest that mTORi can be used in pediatric LT recipients in different clinical situations, both to reinforce immunosuppressive therapy, and to reduce CNI and related toxicity.

Sections du résumé

BACKGROUND
During the past decade, mTOR inhibitors (mTORi), everolimus and sirolimus, have been increasingly used after adult liver transplantation (LT). The aim of the present study was to describe the use of mTORi in pediatric LT recipients.
METHODS
All pediatric LT recipients who received mTORi before December 2017 from 4 European pediatric LT centers were included and analyzed.
RESULTS
The present retrospective study included 30 patients; 21 were male (70%), median age was 9.3 years (range: 1.2-17.1 years) at mTORi introduction. Main indications for mTORi introduction were pre-existing liver malignancy (43.3%), calcineurin inhibitor (CNI) nephrotoxicity (26.7%), or rejection (23.4%). At last follow-up, mTORi CNIs were withdrawn in 10 patients (10/29, 34.5%). The median dose of mTORi was 1.8 mg/day (range: 0.3-5.0) or 0.058 mg/kg/day (range: 0.01-0.26), and the median trough level was 5.1 μg/L (range: 1.0-15.5). After a median follow-up of 2.8 years (range: 0.2-10.0), 50.0% of the patients presented with at least one adverse event. The main adverse events included hyperlipidemia, proteinuria, dermatitis, and mucitis. Overall mTORi discontinuation rate was 23.3% (10.0% because of adverse event). Introduction of mTORi had no significant impact on renal function.
CONCLUSION
Our results suggest that mTORi can be used in pediatric LT recipients in different clinical situations, both to reinforce immunosuppressive therapy, and to reduce CNI and related toxicity.

Identifiants

pubmed: 30528864
pii: S2210-7401(18)30267-5
doi: 10.1016/j.clinre.2018.11.010
pii:
doi:

Substances chimiques

Immunosuppressive Agents 0
Steroids 0
Cyclosporine 83HN0GTJ6D
Everolimus 9HW64Q8G6G
MTOR protein, human EC 2.7.1.1
TOR Serine-Threonine Kinases EC 2.7.11.1
Sirolimus W36ZG6FT64
Tacrolimus WM0HAQ4WNM

Types de publication

Journal Article Multicenter Study

Langues

eng

Sous-ensembles de citation

IM

Pagination

403-409

Informations de copyright

Copyright © 2018 Elsevier Masson SAS. All rights reserved.

Auteurs

Jérôme Dumortier (J)

Department of digestive diseases, Edouard-Herriot hospital, hospices civils de Lyon, 69437 Lyon, France; University of Lyon, 69008 Lyon, France. Electronic address: jerome.dumortier@chu-lyon.fr.

Eduardo Couchonnal (E)

Department of pediatric hepatogastroenterolgy and nutrition, Femme-Mère-Enfant hospital, hospices civils de Lyon, 69677 Lyon, France.

Florence Lacaille (F)

Pediatric hepatology unit, National reference centre for rare pediatric liver diseases, department of pediatric gastroenterology and hepatology, Necker Enfants-Malades hospital, assistance publique-hôpitaux de Paris, 75015 Paris, France.

Christine Rivet (C)

Department of pediatric hepatogastroenterolgy and nutrition, Femme-Mère-Enfant hospital, hospices civils de Lyon, 69677 Lyon, France.

Dominique Debray (D)

Pediatric hepatology unit, National reference centre for rare pediatric liver diseases, department of pediatric gastroenterology and hepatology, Necker Enfants-Malades hospital, assistance publique-hôpitaux de Paris, 75015 Paris, France; University Paris V, 75006 Paris, France.

Olivier Boillot (O)

Department of digestive diseases, Edouard-Herriot hospital, hospices civils de Lyon, 69437 Lyon, France; University of Lyon, 69008 Lyon, France.

Alain Lachaux (A)

University of Lyon, 69008 Lyon, France; Department of pediatric hepatogastroenterolgy and nutrition, Femme-Mère-Enfant hospital, hospices civils de Lyon, 69677 Lyon, France.

Oanez Ackermann (O)

Pediatric hepatology and pediatric liver transplantation unit, National reference centre for rare pediatric liver diseases, hepatinov, Bicêtre hospital, assistance publique-hôpitaux de Paris, 94270 Le Kremlin Bicêtre, France.

Emmanuel Gonzales (E)

Pediatric hepatology and pediatric liver transplantation unit, National reference centre for rare pediatric liver diseases, hepatinov, Bicêtre hospital, assistance publique-hôpitaux de Paris, 94270 Le Kremlin Bicêtre, France; University of Paris-Sud 11, 91400 Paris, France.

Barbara E Wildhaber (BE)

Swiss center for liver disease in children, university hospitals Geneva, 1205 Geneva, Switzerland.

Emmanuel Jacquemin (E)

Pediatric hepatology and pediatric liver transplantation unit, National reference centre for rare pediatric liver diseases, hepatinov, Bicêtre hospital, assistance publique-hôpitaux de Paris, 94270 Le Kremlin Bicêtre, France; University of Paris-Sud 11, 91400 Paris, France.

Valérie McLin (V)

Swiss center for liver disease in children, university hospitals Geneva, 1205 Geneva, Switzerland.

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Classifications MeSH