In Vitro Seeding Activity of Glycoform-Deficient Prions from Variably Protease-Sensitive Prionopathy and Familial CJD Associated with PrP
Humanized transgenic mice
Polymorphism
Prion
Prion disease
Real-time quaking-induced conversion (RT-QuIC)
Serial protein misfolding cyclic amplification (sPMCA)
Variably protease-sensitive prionopathy (VPSPr)
Journal
Molecular neurobiology
ISSN: 1559-1182
Titre abrégé: Mol Neurobiol
Pays: United States
ID NLM: 8900963
Informations de publication
Date de publication:
Aug 2019
Aug 2019
Historique:
received:
12
09
2018
accepted:
17
12
2018
pubmed:
7
1
2019
medline:
18
12
2019
entrez:
7
1
2019
Statut:
ppublish
Résumé
Both sporadic variably protease-sensitive prionopathy (VPSPr) and familial Creutzfeldt-Jakob disease linked to the prion protein (PrP) V180I mutation (fCJD
Identifiants
pubmed: 30612334
doi: 10.1007/s12035-018-1459-0
pii: 10.1007/s12035-018-1459-0
pmc: PMC6614145
doi:
Substances chimiques
Prion Proteins
0
Peptide Hydrolases
EC 3.4.-
Types de publication
Journal Article
Langues
eng
Sous-ensembles de citation
IM
Pagination
5456-5469Subventions
Organisme : NINDS NIH HHS
ID : R01 NS109532
Pays : United States
Organisme : NINDS NIH HHS
ID : R01 NS062787
Pays : United States
Organisme : NINDS NIH HHS
ID : R21 NS087588
Pays : United States
Organisme : NIH HHS
ID : NS087588
Pays : United States
Organisme : NINDS NIH HHS
ID : R01 NS088604
Pays : United States
Commentaires et corrections
Type : ErratumIn
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