Malformations of the lateral semicircular canal correlated with data from the audiogram.
Adult
Audiometry
/ methods
Congenital Abnormalities
/ epidemiology
Female
France
/ epidemiology
Hearing Loss, Conductive
/ diagnosis
Hearing Loss, Sensorineural
/ diagnosis
Humans
Male
Patient Care Management
/ methods
Prevalence
Retrospective Studies
Semicircular Canals
/ abnormalities
Temporal Bone
/ diagnostic imaging
Tomography, X-Ray Computed
/ methods
Audiogram
Congenital
Hearing loss
Lateral semicircular canal
Malformation
Journal
European archives of oto-rhino-laryngology : official journal of the European Federation of Oto-Rhino-Laryngological Societies (EUFOS) : affiliated with the German Society for Oto-Rhino-Laryngology - Head and Neck Surgery
ISSN: 1434-4726
Titre abrégé: Eur Arch Otorhinolaryngol
Pays: Germany
ID NLM: 9002937
Informations de publication
Date de publication:
Apr 2019
Apr 2019
Historique:
received:
30
10
2018
accepted:
12
01
2019
pubmed:
7
2
2019
medline:
21
5
2019
entrez:
7
2
2019
Statut:
ppublish
Résumé
Lateral semicircular canal (LSCC) malformations are one of the most common inner ear malformations. The purpose of this study is to analyze the prevalence and type of hearing losses associated with LSCC malformations, compared to a control group. We retrospectively included 109 patients (166 ears) presenting with a CT-confirmed LSCC malformation, compared to a control group (24 patients). The bony island surface and the width of the inner portion of the LSCC were measured to confirm the malformation. There results were correlated to audiogram data: sensorineural (SHNL), mixed (MHL) or conductive hearing loss (CHL) by an otologist. In the LSCC group, 60.9% of patients presented with an audiogram-confirmed hearing loss, especially SNHL (39.2%, n = 65) and MHL (12.7%, n = 21). Hearing was normal in 39.2% (n = 65) of the cases. Bilateral LSCC malformations (n = 57) were frequently associated with hearing loss (80.7%), SNHL in most of the cases (33.3%). Unilateral LSCC malformations were associated with hearing alterations (51.9%, n = 27), but we also observed a high rate (81%, n = 42) of contralateral abnormalities of the audiogram. LSCC malformations are commonly associated with hearing loss (61%), especially SHNL (39%). The high rate (81%) of contralateral hearing disturbances in unilateral LSCC malformations should be taken into account in the patient's daily life to avoid triggering or exacerbating any hearing loss. Otologists and radiologists must cooperate to ensure that all malformations are correctly described on CT, especially to improve the patient's education regarding hearing preservation.
Identifiants
pubmed: 30725208
doi: 10.1007/s00405-019-05294-y
pii: 10.1007/s00405-019-05294-y
doi:
Types de publication
Journal Article
Langues
eng
Sous-ensembles de citation
IM
Pagination
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