A nutrition-based approach to epidermolysis bullosa: Causes, assessments, requirements and management.
Enteral nutrition
Epidermolysis bullosa
Growth retardation
Hypercatabolism
Nutritional status
Undernutrition
Journal
Clinical nutrition (Edinburgh, Scotland)
ISSN: 1532-1983
Titre abrégé: Clin Nutr
Pays: England
ID NLM: 8309603
Informations de publication
Date de publication:
02 2020
02 2020
Historique:
received:
14
08
2018
revised:
23
01
2019
accepted:
15
02
2019
pubmed:
13
3
2019
medline:
14
8
2021
entrez:
13
3
2019
Statut:
ppublish
Résumé
Inherited epidermolysis bullosa (EB) is a clinically and genetically heterogeneous group of rare diseases characterized by skin and mucous membrane fragility. EB primarily involves the skin and, in specific subtypes, the mucous membrane, resulting in complications which can strongly affect nutritional status (e.g. gastrointestinal complications, hand deformities, pain). The aims of nutritional support mainly include improving nutritional status, alleviating the stress of oral feeding and minimizing nutritional deficiencies, thus consequently improving growth, pubertal development, bowel function, immune status and wound healing. The aim of this review is to discuss knowledge of different aspects of the disease related to nutrition and growth.
Identifiants
pubmed: 30857908
pii: S0261-5614(19)30077-9
doi: 10.1016/j.clnu.2019.02.023
pii:
doi:
Types de publication
Journal Article
Research Support, Non-U.S. Gov't
Review
Langues
eng
Sous-ensembles de citation
IM
Pagination
343-352Informations de copyright
Copyright © 2019 Elsevier Ltd and European Society for Clinical Nutrition and Metabolism. All rights reserved.