Active PI3K abrogates central tolerance in high-avidity autoreactive B cells.


Journal

The Journal of experimental medicine
ISSN: 1540-9538
Titre abrégé: J Exp Med
Pays: United States
ID NLM: 2985109R

Informations de publication

Date de publication:
06 05 2019
Historique:
received: 27 08 2018
revised: 23 01 2019
accepted: 22 03 2019
pubmed: 6 4 2019
medline: 6 5 2020
entrez: 6 4 2019
Statut: ppublish

Résumé

Autoreactive B cells that bind self-antigen with high avidity in the bone marrow undergo mechanisms of central tolerance that prevent their entry into the peripheral B cell population. These mechanisms are breached in many autoimmune patients, increasing their risk of B cell-mediated autoimmune diseases. Resolving the molecular pathways that can break central B cell tolerance could therefore provide avenues to diminish autoimmunity. Here, we show that B cell-intrinsic expression of a constitutively active form of PI3K-P110α by high-avidity autoreactive B cells of mice completely abrogates central B cell tolerance and further promotes these cells to escape from the bone marrow, differentiate in peripheral tissue, and undergo activation in response to self-antigen. Upon stimulation with T cell help factors, these B cells secrete antibodies in vitro but remain unable to secrete autoantibodies in vivo. Overall, our data demonstrate that activation of the PI3K pathway leads high-avidity autoreactive B cells to breach central, but not late, stages of peripheral tolerance.

Identifiants

pubmed: 30948496
pii: jem.20181652
doi: 10.1084/jem.20181652
pmc: PMC6504226
doi:

Substances chimiques

Autoantibodies 0
Autoantigens 0
Receptors, Antigen, B-Cell 0
Receptors, Complement 3d 0
Class Ia Phosphatidylinositol 3-Kinase EC 2.7.1.137

Types de publication

Journal Article Research Support, N.I.H., Extramural

Langues

eng

Sous-ensembles de citation

IM

Pagination

1135-1153

Subventions

Organisme : NIAID NIH HHS
ID : R21 AI131639
Pays : United States
Organisme : NIAID NIH HHS
ID : R01 AI136534
Pays : United States
Organisme : NCI NIH HHS
ID : P30 CA046934
Pays : United States
Organisme : NIAID NIH HHS
ID : R56 AI052310
Pays : United States
Organisme : NIAID NIH HHS
ID : R01 AI052310
Pays : United States

Informations de copyright

© 2019 Greaves et al.

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Auteurs

Sarah A Greaves (SA)

Department of Immunology and Microbiology, University of Colorado School of Medicine, Anschutz Medical Campus, Aurora, CO.

Jacob N Peterson (JN)

Department of Immunology and Microbiology, University of Colorado School of Medicine, Anschutz Medical Campus, Aurora, CO.

Pamela Strauch (P)

Department of Immunology and Microbiology, University of Colorado School of Medicine, Anschutz Medical Campus, Aurora, CO.

Raul M Torres (RM)

Department of Immunology and Microbiology, University of Colorado School of Medicine, Anschutz Medical Campus, Aurora, CO.
Department of Biomedical Research, National Jewish Health, Denver, CO.

Roberta Pelanda (R)

Department of Immunology and Microbiology, University of Colorado School of Medicine, Anschutz Medical Campus, Aurora, CO roberta.pelanda@ucdenver.edu.
Department of Biomedical Research, National Jewish Health, Denver, CO.

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Classifications MeSH