Heterogeneity and Architecture of Pathological Prion Protein Assemblies: Time to Revisit the Molecular Basis of the Prion Replication Process?


Journal

Viruses
ISSN: 1999-4915
Titre abrégé: Viruses
Pays: Switzerland
ID NLM: 101509722

Informations de publication

Date de publication:
10 05 2019
Historique:
received: 17 04 2019
revised: 07 05 2019
accepted: 08 05 2019
entrez: 15 5 2019
pubmed: 15 5 2019
medline: 25 7 2020
Statut: epublish

Résumé

Prions are proteinaceous infectious agents responsible for a range of neurodegenerative diseases in animals and humans. Prion particles are assemblies formed from a misfolded, β-sheet rich, aggregation-prone isoform (PrP

Identifiants

pubmed: 31083283
pii: v11050429
doi: 10.3390/v11050429
pmc: PMC6563208
pii:
doi:

Substances chimiques

PrPC Proteins 0
PrPSc Proteins 0

Types de publication

Journal Article Research Support, Non-U.S. Gov't Review

Langues

eng

Sous-ensembles de citation

IM

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Auteurs

Angélique Igel-Egalon (A)

Molecular Virology and Immunology Unit (VIM), INRA, Université Paris-Saclay, 78350 Jouy-en-Josas, France. angelique.egalon@inra.fr.

Jan Bohl (J)

Molecular Virology and Immunology Unit (VIM), INRA, Université Paris-Saclay, 78350 Jouy-en-Josas, France. jan.bohl@u-psud.fr.
Laboratory of Physical Chemistry (LCP), UMR 8000 CNRS, Université Paris Sud, 91400 Orsay, France. jan.bohl@u-psud.fr.

Mohammed Moudjou (M)

Molecular Virology and Immunology Unit (VIM), INRA, Université Paris-Saclay, 78350 Jouy-en-Josas, France. mohammed.moudjou@inra.fr.

Laetitia Herzog (L)

Molecular Virology and Immunology Unit (VIM), INRA, Université Paris-Saclay, 78350 Jouy-en-Josas, France. laetitia.herzog@inra.fr.

Fabienne Reine (F)

Molecular Virology and Immunology Unit (VIM), INRA, Université Paris-Saclay, 78350 Jouy-en-Josas, France. fabienne.reine@inra.fr.

Human Rezaei (H)

Molecular Virology and Immunology Unit (VIM), INRA, Université Paris-Saclay, 78350 Jouy-en-Josas, France. human.rezaei@inra.fr.

Vincent Béringue (V)

Molecular Virology and Immunology Unit (VIM), INRA, Université Paris-Saclay, 78350 Jouy-en-Josas, France. vincent.beringue@inra.fr.

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