Hydroxychloroquine-induced podocytopathy mimicking Fabry disease.


Journal

BMJ case reports
ISSN: 1757-790X
Titre abrégé: BMJ Case Rep
Pays: England
ID NLM: 101526291

Informations de publication

Date de publication:
13 May 2019
Historique:
entrez: 16 5 2019
pubmed: 16 5 2019
medline: 25 12 2019
Statut: epublish

Résumé

Hydroxychloroquine (HCQ) is largely prescribed as an immunomodulator to prevent systemic diseases flares in patients with systemic lupus erythematous, rheumatoid arthritis, Sjogren's disease. Among reported side effects, HCQ can accumulate in lysosomes and induced phospholipidosis. Here, we report an HCQ-induced podocytopathy mimicking Fabry disease (FD). They share the same histological lesions: cytoplasmic vacuolisation of the podocytes and zebra bodies on light and electronic microscopy. FD has been ruled out by measuring enzymatic activity and genetic test. The persistence of proteinuria after immunological remission of a systemic disease treated with HCQ could suggest this HCQ-induced podocytopathy.

Identifiants

pubmed: 31088818
pii: 12/5/e228876
doi: 10.1136/bcr-2018-228876
pmc: PMC6536225
pii:
doi:

Substances chimiques

Antirheumatic Agents 0
Hydroxychloroquine 4QWG6N8QKH

Types de publication

Case Reports Journal Article

Langues

eng

Sous-ensembles de citation

IM

Informations de copyright

© BMJ Publishing Group Limited 2019. No commercial re-use. See rights and permissions. Published by BMJ.

Déclaration de conflit d'intérêts

Competing interests: None declared.

Références

Presse Med. 2014 Jun;43(6 Pt 2):e167-80
pubmed: 24855048
BMC Nephrol. 2017 May 12;18(1):157
pubmed: 28499424
Nephrol Dial Transplant. 2007 Oct;22(10):3074-7
pubmed: 17623715
Hum Pathol. 2003 Mar;34(3):285-9
pubmed: 12673565
Ultrastruct Pathol. 2013 Apr;37(2):146-50
pubmed: 23573895
Kidney Int. 2018 Sep;94(3):634
pubmed: 30143072
Clin Kidney J. 2013 Oct;6(5):533-6
pubmed: 26120446
J Am Soc Nephrol. 2002 Jun;13 Suppl 2:S134-8
pubmed: 12068025
Mod Pathol. 2005 May;18(5):733-8
pubmed: 15605079
Clin J Am Soc Nephrol. 2018 May 7;13(5):702-709
pubmed: 29661770
Am J Kidney Dis. 2006 Nov;48(5):844-50
pubmed: 17060007

Auteurs

Justine Serre (J)

Nephrology, Assistance Publique - Hôpitaux de Paris, Paris, France.

David Buob (D)

Pathology, Assistance Publique - Hôpitaux de paris, Paris, France.
UMRS 1155, Sorbonne Université INSERM, Paris, France.

Jean-Jacques Boffa (JJ)

Nephrology, Assistance Publique - Hôpitaux de Paris, Paris, France.
UMRS 1155, Sorbonne Université INSERM, Paris, France.

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Classifications MeSH