Pregnancy-associated plasma protein-aa supports hair cell survival by regulating mitochondrial function.
Animals
Animals, Genetically Modified
Calcium
/ metabolism
Cell Survival
/ genetics
Green Fluorescent Proteins
/ genetics
Hair Cells, Auditory
/ cytology
Humans
Larva
/ genetics
Metalloendopeptidases
/ genetics
Microscopy, Confocal
Mitochondria
/ genetics
Mutation
Pregnancy-Associated Plasma Protein-A
/ genetics
Reactive Oxygen Species
/ metabolism
Zebrafish
/ genetics
Zebrafish Proteins
/ genetics
IGF signaling
cell biology
hair cell
mitochondria
neuroscience
oxidative stress
pregnancy associated plasma protein a
zebrafish
Journal
eLife
ISSN: 2050-084X
Titre abrégé: Elife
Pays: England
ID NLM: 101579614
Informations de publication
Date de publication:
17 06 2019
17 06 2019
Historique:
received:
22
03
2019
accepted:
14
06
2019
pubmed:
18
6
2019
medline:
26
2
2020
entrez:
18
6
2019
Statut:
epublish
Résumé
To support cell survival, mitochondria must balance energy production with oxidative stress. Inner ear hair cells are particularly vulnerable to oxidative stress; thus require tight mitochondrial regulation. We identified a novel molecular regulator of the hair cells' mitochondria and survival: Pregnancy-associated plasma protein-aa (Pappaa). Hair cells in zebrafish
Identifiants
pubmed: 31205004
doi: 10.7554/eLife.47061
pii: 47061
pmc: PMC6594750
doi:
pii:
Substances chimiques
Reactive Oxygen Species
0
Zebrafish Proteins
0
Green Fluorescent Proteins
147336-22-9
PAPPA2 protein, human
EC 3.4.-
Metalloendopeptidases
EC 3.4.24.-
Pregnancy-Associated Plasma Protein-A
EC 3.4.24.-
pappaa protein, zebrafish
EC 3.4.24.-
Calcium
SY7Q814VUP
Types de publication
Journal Article
Research Support, Non-U.S. Gov't
Langues
eng
Sous-ensembles de citation
IM
Informations de copyright
© 2019, Alassaf et al.
Déclaration de conflit d'intérêts
MA, ED, JM, MW No competing interests declared
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