Cardiovascular manifestations of myotonic dystrophy.
Animals
Arrhythmias, Cardiac
/ genetics
Cardiac Pacing, Artificial
/ adverse effects
Death, Sudden, Cardiac
/ epidemiology
Defibrillators, Implantable
Electric Countershock
/ adverse effects
Genetic Predisposition to Disease
Humans
Myotonic Dystrophy
/ epidemiology
Pacemaker, Artificial
Prevalence
Risk Factors
Treatment Outcome
Journal
Trends in cardiovascular medicine
ISSN: 1873-2615
Titre abrégé: Trends Cardiovasc Med
Pays: United States
ID NLM: 9108337
Informations de publication
Date de publication:
05 2020
05 2020
Historique:
received:
26
09
2018
revised:
03
06
2019
accepted:
04
06
2019
pubmed:
20
6
2019
medline:
22
10
2020
entrez:
20
6
2019
Statut:
ppublish
Résumé
Patients with myotonic dystrophy, the most common neuromuscular dystrophy in adults, have a high prevalence of arrhythmic complications with increased cardiovascular mortality and high risk for sudden death. Sudden death prevention is central and relies on annual follow-up and prophylactic permanent pacing in patients with conduction defects on electrocardiogram and/or infrahisian blocks on electrophysiological study. Implantable cardiac defibrillator therapy may be indicated in patients with ventricular tachyarrhythmia.
Identifiants
pubmed: 31213350
pii: S1050-1738(18)30224-X
doi: 10.1016/j.tcm.2019.06.001
pii:
doi:
Types de publication
Journal Article
Review
Langues
eng
Sous-ensembles de citation
IM
Pagination
232-238Commentaires et corrections
Type : CommentIn
Informations de copyright
Copyright © 2019 The Authors. Published by Elsevier Inc. All rights reserved.