Correlation between Papilledema and Intracranial Hypertension in Crouzon Syndrome: A Case Report and Review of the Literature.
Craniosynostosis
Crouzon syndrome
Intracranial hypertension
Papilledema
Journal
Pediatric neurosurgery
ISSN: 1423-0305
Titre abrégé: Pediatr Neurosurg
Pays: Switzerland
ID NLM: 9114967
Informations de publication
Date de publication:
2019
2019
Historique:
received:
28
12
2018
accepted:
05
05
2019
pubmed:
4
7
2019
medline:
24
1
2020
entrez:
4
7
2019
Statut:
ppublish
Résumé
Crouzon syndrome represents the most common syndromic craniosynostosis. Ocular complications are frequent, including papilledema and optic atrophy, often related to increased intracranial pressure (ICP). However, there is a poor correlation between ICP normalization and resolution of papilledema. We describe the case of a 6-month-old infant who presented with typical phenotypic features of Crouzon syndrome. Pre- and postoperative ICP monitoring was used. Papilledema persisted despite ICP improvement after decompressive craniectomy. Possible causes of papilledema in this syndromic craniosynostosis are discussed in light of the existing literature.
Identifiants
pubmed: 31269504
pii: 000500767
doi: 10.1159/000500767
doi:
Types de publication
Case Reports
Journal Article
Review
Langues
eng
Sous-ensembles de citation
IM
Pagination
223-227Informations de copyright
© 2019 S. Karger AG, Basel.