Adenosine A
Animals
Autophagy
Cell Differentiation
Cholesterol
/ metabolism
Cyclic AMP
/ metabolism
Cyclic AMP-Dependent Protein Kinases
/ metabolism
Fibroblasts
/ metabolism
Humans
Mitochondria
/ metabolism
Niemann-Pick Disease, Type C
/ etiology
Oligodendroglia
/ metabolism
Receptor, Adenosine A2A
/ metabolism
Journal
Scientific reports
ISSN: 2045-2322
Titre abrégé: Sci Rep
Pays: England
ID NLM: 101563288
Informations de publication
Date de publication:
05 07 2019
05 07 2019
Historique:
received:
10
12
2018
accepted:
10
05
2019
entrez:
7
7
2019
pubmed:
7
7
2019
medline:
23
10
2020
Statut:
epublish
Résumé
Niemann Pick type C (NPC) disease is a rare neurovisceral disorder. Mutations in npc1 gene induce an intracellular accumulation of unesterified cholesterol in the endosomal/lysosomal system causing cell death. We recently showed that stimulation of adenosine A
Identifiants
pubmed: 31278313
doi: 10.1038/s41598-019-46268-8
pii: 10.1038/s41598-019-46268-8
pmc: PMC6611770
doi:
Substances chimiques
Receptor, Adenosine A2A
0
Cholesterol
97C5T2UQ7J
Cyclic AMP
E0399OZS9N
Cyclic AMP-Dependent Protein Kinases
EC 2.7.11.11
Types de publication
Journal Article
Research Support, Non-U.S. Gov't
Langues
eng
Sous-ensembles de citation
IM
Pagination
9782Références
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