[Waldenström macroglobulinaemia].
Maladie de Waldenström.
Adenine
/ analogs & derivatives
Age of Onset
Aged
DNA Mutational Analysis
/ methods
Frail Elderly
Humans
Molecular Diagnostic Techniques
/ methods
Molecular Targeted Therapy
/ methods
Myeloid Differentiation Factor 88
/ genetics
Piperidines
Pyrazoles
/ therapeutic use
Pyrimidines
/ therapeutic use
Waldenstrom Macroglobulinemia
/ diagnosis
Journal
Presse medicale (Paris, France : 1983)
ISSN: 2213-0276
Titre abrégé: Presse Med
Pays: France
ID NLM: 8302490
Informations de publication
Date de publication:
Historique:
pubmed:
25
8
2019
medline:
24
9
2019
entrez:
25
8
2019
Statut:
ppublish
Résumé
Lymphoplasmocytic lymphona with monoclonal lgM, rare. Median age at diagnosis 70 years old, frail population. Heterogenous clinic presentation. Molecular diagnosis with MYD88. Treatment required for symptomatic WM patients only. 1st line therapy: DRC. Input of targeted therapies (ibrutinib) for frail patients, maintenance effect.
Identifiants
pubmed: 31444019
pii: S0755-4982(19)30310-0
doi: 10.1016/j.lpm.2019.07.020
pii:
doi:
Substances chimiques
MYD88 protein, human
0
Myeloid Differentiation Factor 88
0
Piperidines
0
Pyrazoles
0
Pyrimidines
0
ibrutinib
1X70OSD4VX
Adenine
JAC85A2161
Types de publication
Journal Article
Review
Langues
fre
Sous-ensembles de citation
IM
Pagination
832-841Informations de copyright
Copyright © 2019. Published by Elsevier Masson SAS.