Ankle bracing practices in ambulatory, corticosteroid-naive boys with Duchenne muscular dystrophy.
Duchenne muscular dystrophy
bracing
corticosteroids
dynamic ankle-foot orthoses
pediatrics
static ankle-foot orthoses
Journal
Muscle & nerve
ISSN: 1097-4598
Titre abrégé: Muscle Nerve
Pays: United States
ID NLM: 7803146
Informations de publication
Date de publication:
01 2020
01 2020
Historique:
received:
16
01
2019
revised:
19
09
2019
accepted:
21
09
2019
pubmed:
8
10
2019
medline:
31
3
2020
entrez:
8
10
2019
Statut:
ppublish
Résumé
Loss of ambulation in Duchenne muscular dystrophy presages scoliosis, respiratory failure, and death. Strategies to maintain ankle range of motion are employed, but little evidence exists to support these approaches and limited information is available concerning current practice. In this study we assessed baseline bracing data from 187 boys participating in a multicenter, international clinical trial. Ankle-foot orthoses (AFOs) were recommended for 54% of the boys, with nighttime static AFOs and nighttime dynamic AFOs utilized in 94% and 6% of these boys, respectively. Daytime static AFOs were recommended for 3 boys. Compliance with bracing recommendations was 54% for nighttime static braces and 67% for nighttime dynamic braces. The basis for the variation in recommended AFO use is unknown and requires further study. Long-term follow-up of boys may permit assessment of the effects of AFO use.
Types de publication
Journal Article
Multicenter Study
Randomized Controlled Trial
Research Support, N.I.H., Extramural
Research Support, Non-U.S. Gov't
Langues
eng
Sous-ensembles de citation
IM
Pagination
52-57Subventions
Organisme : NINDS NIH HHS
ID : U01 NS061795
Pays : United States
Organisme : NINDS NIH HHS
ID : U01 NS061799
Pays : United States
Informations de copyright
© 2019 Wiley Periodicals, Inc.
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