Multiple co-existing antibodies in autoimmune encephalitis: A case and review of the literature.
Autoimmune encephalitis
Co-existing autoantibodies
Paraneoplastic syndrome
Journal
Journal of neuroimmunology
ISSN: 1872-8421
Titre abrégé: J Neuroimmunol
Pays: Netherlands
ID NLM: 8109498
Informations de publication
Date de publication:
15 12 2019
15 12 2019
Historique:
received:
11
07
2019
revised:
22
09
2019
accepted:
05
10
2019
pubmed:
28
10
2019
medline:
18
6
2020
entrez:
27
10
2019
Statut:
ppublish
Résumé
A 66-year-old man with a history of chronic tobacco use presented with two months of progressive memory deficits, ataxia, diplopia, and opsoclonus. His brain magnetic resonance imaging (MRI) showed limbic and brainstem encephalitis, and antibody testing was positive for anti-Ma1/Ma2, anti-N-methyl-d-aspartate receptor (anti-NMDA-R) and anti-glutamic acid decarboxylase 65 (anti-GAD65) antibodies. His encephalitis improved with intravenous steroids, plasmapheresis, and rituximab initiation. His PET/CT was suspicious for lung malignancy, but a progressive deterioration of his respiratory status prevented full investigation. Multiple auto-antibodies may be produced in response to a malignancy and overlapping of clinical presentations may occur with multiple auto-antibodies.
Identifiants
pubmed: 31655424
pii: S0165-5728(19)30317-0
doi: 10.1016/j.jneuroim.2019.577084
pii:
doi:
Substances chimiques
Autoantibodies
0
Types de publication
Case Reports
Journal Article
Review
Langues
eng
Sous-ensembles de citation
IM
Pagination
577084Informations de copyright
Copyright © 2019 Elsevier B.V. All rights reserved.