Management of People With a Fontan Circulation: a Cardiac Society of Australia and New Zealand Position statement.


Journal

Heart, lung & circulation
ISSN: 1444-2892
Titre abrégé: Heart Lung Circ
Pays: Australia
ID NLM: 100963739

Informations de publication

Date de publication:
Jan 2020
Historique:
received: 16 09 2019
accepted: 16 09 2019
pubmed: 19 11 2019
medline: 4 6 2020
entrez: 19 11 2019
Statut: ppublish

Résumé

The Fontan circulation describes the circulatory state resulting from an operation in congenital heart disease where systemic venous return is directed to the lungs without an intervening active pumping chamber. As survival increases, so too does recognition of the potential health challenges. This document aims to allow clinicians, people with a Fontan circulation, and their families to benefit from consensus agreement about management of the person with a Fontan circulation. The document was crafted with input from a multidisciplinary group of health care providers as well as individuals with a Fontan circulation and families. It is hoped that the shared common vision of long-term wellbeing will continue to drive improvements in care and quality of life in this patient population and eventually translate into improved survival. KEYPOINTS.

Identifiants

pubmed: 31735685
pii: S1443-9506(19)31458-1
doi: 10.1016/j.hlc.2019.09.010
pii:
doi:

Types de publication

Letter Review

Langues

eng

Sous-ensembles de citation

IM

Pagination

5-39

Informations de copyright

Copyright © 2019 The Authors. Published by Elsevier B.V. All rights reserved.

Auteurs

Dominica Zentner (D)

Department of Cardiology, Royal Melbourne Hospital, Melbourne, Vic, Australia; Murdoch Children's Research Institute, Melbourne, Vic, Australia; Department of Genomic Medicine, Royal Melbourne Hospital, Melbourne, Vic, Australia; Department of Medicine, University of Melbourne, Melbourne, Vic, Australia. Electronic address: dominica.zentner@mh.org.au.

David S Celermajer (DS)

Department of Cardiology, Royal Prince Alfred Hospital, Sydney, NSW, Australia; Faculty of Medicine and Health, University of Sydney, Sydney, NSW, Australia.

Thomas Gentles (T)

Paediatric and Congenital Cardiac Service, Starship Children's Hospital, Auckland, New Zealand.

Yves d'Udekem (Y)

Murdoch Children's Research Institute, Melbourne, Vic, Australia; Department of Cardiac Surgery, Royal Children's Hospital, Melbourne, Vic, Australia; Department of Paediatrics, University of Melbourne, Melbourne, Vic, Australia.

Julian Ayer (J)

Heart Centre for Children, Sydney Children's Hospitals Network, Sydney, NSW, Australia; Sydney Medical School, University of Sydney, Sydney, NSW, Australia.

Gillian M Blue (GM)

Heart Centre for Children, Sydney Children's Hospitals Network, Sydney, NSW, Australia; Sydney Medical School, University of Sydney, Sydney, NSW, Australia.

Cameron Bridgman (C)

Department of Cardiology, Flinders Medical Centre, Adelaide, SA, Australia.

Luke Burchill (L)

Department of Cardiology, Royal Melbourne Hospital, Melbourne, Vic, Australia; Department of Medicine, University of Melbourne, Melbourne, Vic, Australia.

Michael Cheung (M)

Murdoch Children's Research Institute, Melbourne, Vic, Australia; Department of Paediatrics, University of Melbourne, Melbourne, Vic, Australia; Department of Cardiology, Royal Children's Hospital, Melbourne, Vic, Australia.

Rachael Cordina (R)

Department of Cardiology, Royal Prince Alfred Hospital, Sydney, NSW, Australia; Sydney Medical School, University of Sydney, Sydney, NSW, Australia.

Evelyn Culnane (E)

Transition Support Service, Royal Children's Hospital, Melbourne, Vic, Australia.

Andrew Davis (A)

Murdoch Children's Research Institute, Melbourne, Vic, Australia; Department of Paediatrics, University of Melbourne, Melbourne, Vic, Australia; Department of Cardiology, Royal Children's Hospital, Melbourne, Vic, Australia.

Karin du Plessis (K)

Murdoch Children's Research Institute, Melbourne, Vic, Australia; Department of Paediatrics, University of Melbourne, Melbourne, Vic, Australia.

Karen Eagleson (K)

Faculty of Medicine, University of Queensland, Brisbane, Qld, Australia; Queensland Paediatric Cardiac Research, Children's Health Queensland, Brisbane, Qld, Australia.

Kirsten Finucane (K)

Paediatric and Congenital Cardiac Service, Starship Children's Hospital, Auckland, New Zealand.

Belinda Frank (B)

Australian and New Zealand Fontan Advocacy Committee, Australia and New Zealand.

Sebastian Greenway (S)

Paediatric and Congenital Cardiac Service, Starship Children's Hospital, Auckland, New Zealand.

Leeanne Grigg (L)

Department of Cardiology, Royal Melbourne Hospital, Melbourne, Vic, Australia; Department of Medicine, University of Melbourne, Melbourne, Vic, Australia.

Winita Hardikar (W)

Murdoch Children's Research Institute, Melbourne, Vic, Australia; Department of Paediatrics, University of Melbourne, Melbourne, Vic, Australia; Department of Gastroenterology and Clinical Nutrition, Royal Children's Hospital, Melbourne, Vic, Australia.

Tim Hornung (T)

Paediatric and Congenital Cardiac Service, Starship Children's Hospital, Auckland, New Zealand.

Jenny Hynson (J)

Department of Paediatrics, University of Melbourne, Melbourne, Vic, Australia; Victorian Paediatric Palliative Care Program, Royal Children's Hospital, Melbourne, Vic, Australia.

Ajay J Iyengar (AJ)

Murdoch Children's Research Institute, Melbourne, Vic, Australia; Department of Cardiac Surgery, Royal Children's Hospital, Melbourne, Vic, Australia; Department of Paediatrics, University of Melbourne, Melbourne, Vic, Australia.

Paul James (P)

Department of Genomic Medicine, Royal Melbourne Hospital, Melbourne, Vic, Australia; Department of Pathology, University of Melbourne, Melbourne, Vic, Australia.

Robert Justo (R)

Faculty of Medicine, University of Queensland, Brisbane, Qld, Australia; Queensland Paediatric Cardiac Research, Children's Health Queensland, Brisbane, Qld, Australia.

Jonathan Kalman (J)

Department of Cardiology, Royal Melbourne Hospital, Melbourne, Vic, Australia; Department of Medicine, University of Melbourne, Melbourne, Vic, Australia.

Nadine Kasparian (N)

Heart Centre for Children, Sydney Children's Hospitals Network, Sydney, NSW, Australia; Discipline of Paediatrics, School of Women's and Children's Health, UNSW Medicine, University of New South Wales, Sydney, NSW, Australia.

Brian Le (B)

Department of Medicine, University of Melbourne, Melbourne, Vic, Australia; Palliative Care, Royal Melbourne Hospital, Melbourne, Vic, Australia.

Kate Marshall (K)

Heart Centre for Children, Sydney Children's Hospitals Network, Sydney, NSW, Australia; Discipline of Paediatrics, School of Women's and Children's Health, UNSW Medicine, University of New South Wales, Sydney, NSW, Australia.

Jacob Mathew (J)

Murdoch Children's Research Institute, Melbourne, Vic, Australia; Department of Cardiology, Royal Children's Hospital, Melbourne, Vic, Australia.

David McGiffin (D)

Department of Cardiothoracic Surgery, Alfred Health, Melbourne, Vic, Australia; Department of Surgery, Monash University, Melbourne, Vic, Australia.

Mark McGuire (M)

Department of Cardiology, Royal Prince Alfred Hospital, Sydney, NSW, Australia; Sydney Medical School, University of Sydney, Sydney, NSW, Australia.

Paul Monagle (P)

Murdoch Children's Research Institute, Melbourne, Vic, Australia; Department of Paediatrics, University of Melbourne, Melbourne, Vic, Australia; Department of Haematology, Royal Children's Hospital, Melbourne, Vic, Australia.

Ben Moore (B)

Department of Cardiology, Royal Prince Alfred Hospital, Sydney, NSW, Australia; Sydney Medical School, University of Sydney, Sydney, NSW, Australia.

Julie Neilsen (J)

Heart Kids NZ, Auckland, New Zealand.

Bernadette O'Connor (B)

llied Health, Royal Children's Hospital, Melbourne, Vic, Australia.

Clare O'Donnell (C)

Paediatric and Congenital Cardiac Service, Starship Children's Hospital, Auckland, New Zealand.

Andreas Pflaumer (A)

Murdoch Children's Research Institute, Melbourne, Vic, Australia; Department of Paediatrics, University of Melbourne, Melbourne, Vic, Australia; Department of Cardiology, Royal Children's Hospital, Melbourne, Vic, Australia.

Kathryn Rice (K)

Paediatric and Congenital Cardiac Service, Starship Children's Hospital, Auckland, New Zealand.

Gary Sholler (G)

Heart Centre for Children, Sydney Children's Hospitals Network, Sydney, NSW, Australia; Sydney Medical School, University of Sydney, Sydney, NSW, Australia.

Jonathan R Skinner (JR)

Paediatric and Congenital Cardiac Service, Starship Children's Hospital, Auckland, New Zealand.

Siddharth Sood (S)

Department of Medicine, University of Melbourne, Melbourne, Vic, Australia; Department of Gastroenterology and Hepatology, Royal Melbourne Hospital, Melbourne, Vic, Australia.

Juliet Ward (J)

Department of Cardiology, Royal Melbourne Hospital, Melbourne, Vic, Australia.

Robert Weintraub (R)

Murdoch Children's Research Institute, Melbourne, Vic, Australia; Department of Paediatrics, University of Melbourne, Melbourne, Vic, Australia; Department of Cardiology, Royal Children's Hospital, Melbourne, Vic, Australia.

Tom Wilson (T)

Murdoch Children's Research Institute, Melbourne, Vic, Australia; Department of Paediatrics, University of Melbourne, Melbourne, Vic, Australia.

William Wilson (W)

Department of Cardiology, Royal Melbourne Hospital, Melbourne, Vic, Australia; Department of Medicine, University of Melbourne, Melbourne, Vic, Australia.

David Winlaw (D)

Faculty of Medicine and Health, University of Sydney, Sydney, NSW, Australia; Heart Centre for Children, Sydney Children's Hospitals Network, Sydney, NSW, Australia.

Angela Wood (A)

Department of Cardiology, Royal Children's Hospital, Melbourne, Vic, Australia; ongenital Heart Alliance of Australia and New Zealand Registry Board, Melbourne, Vic, Australia.

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Classifications MeSH