Pulmonary emphysema not combined with lung fibrosis in systemic sclerosis.
Emphysema
High Resolution Computed Tomography
Interstitial lung disease
Systemic Sclerosis
Journal
Respiratory medicine
ISSN: 1532-3064
Titre abrégé: Respir Med
Pays: England
ID NLM: 8908438
Informations de publication
Date de publication:
Historique:
received:
14
07
2019
revised:
06
11
2019
accepted:
07
11
2019
pubmed:
19
11
2019
medline:
20
8
2020
entrez:
19
11
2019
Statut:
ppublish
Résumé
Interstitial Lung Disease (ILD) is a common finding of Systemic Sclerosis (SSc) mainly presenting in the form of Nonspecific Interstitial Pneumonia (NSIP) and deeply affecting patients' prognosis. Beside NSIP, other types of ILD have been reported. The most recently described pattern is the so-called Combined-pulmonary emphysema and lung fibrosis, characterized by the coexistence of both upper lobes centrilobular and paraseptal emphysema and lower lobes ILD. We presented three cases of patients with SSc, in which High Resolution Computed Tomography examinations showed emphysema with atypical distribution and radiological presentation, without or with mild signs of fibrosing lung disease, that stabilized after immunosuppressive treatment.
Identifiants
pubmed: 31739247
pii: S0954-6111(19)30330-0
doi: 10.1016/j.rmed.2019.105816
pii:
doi:
Substances chimiques
Immunosuppressive Agents
0
Types de publication
Journal Article
Langues
eng
Sous-ensembles de citation
IM
Pagination
105816Informations de copyright
Copyright © 2019. Published by Elsevier Ltd.