Identification and typing of cardiac amyloidosis by noninvasive imaging: Two cases for two patterns.
Aged, 80 and over
Albuminuria
/ complications
Amyloid
/ analysis
Amyloidosis
/ diagnostic imaging
Angina, Unstable
/ diagnostic imaging
Biopsy
Diphosphonates
Electrocardiography
Heart Diseases
/ diagnostic imaging
Humans
Hypertension
/ complications
Magnetic Resonance Imaging
Male
Middle Aged
Myocardium
/ pathology
Nephrotic Syndrome
/ complications
Prognosis
Radionuclide Imaging
Systole
Technetium Compounds
Amyloidosis
CZT
SPECT
Journal
Journal of nuclear cardiology : official publication of the American Society of Nuclear Cardiology
ISSN: 1532-6551
Titre abrégé: J Nucl Cardiol
Pays: United States
ID NLM: 9423534
Informations de publication
Date de publication:
06 2020
06 2020
Historique:
received:
05
11
2019
accepted:
26
11
2019
pubmed:
18
12
2019
medline:
31
8
2021
entrez:
18
12
2019
Statut:
ppublish
Résumé
Cardiac amyloidosis is a restrictive infiltrative cardiomyopathy burdened by high mortality. The two more common forms are immunoglobulin light-chain amyloidosis and transthyretin-related amyloidosis with different prognoses and treatments. However, distinguishing between them is challenging. Appropriate utilization of the different available imaging techniques in the evaluation of patients with known or suspected cardiac amyloidosis is mandatory. We report two cases with cardiac amyloidosis of different etiology and with distinct imaging patterns. In the first case, the negative
Identifiants
pubmed: 31845305
doi: 10.1007/s12350-019-01982-8
pii: 10.1007/s12350-019-01982-8
doi:
Substances chimiques
Amyloid
0
Diphosphonates
0
Technetium Compounds
0
technetium Tc 99m diphosphonate
8V3FGC4J77
Types de publication
Case Reports
Journal Article
Langues
eng
Sous-ensembles de citation
IM