Recurrent chromosomal rearrangements of


Journal

Gut
ISSN: 1468-3288
Titre abrégé: Gut
Pays: England
ID NLM: 2985108R

Informations de publication

Date de publication:
09 2020
Historique:
received: 04 09 2019
revised: 27 11 2019
accepted: 14 12 2019
pubmed: 8 1 2020
medline: 7 4 2021
entrez: 8 1 2020
Statut: ppublish

Résumé

Inflammatory hepatocellular adenomas (IHCAs) are benign liver tumours characterised by an activation of the janus kinase (JAK)/signal transducers and activators of transcription (STAT) pathway caused by oncogenic activating mutations. However, a subset of IHCA lacks of identified mutation explaining the inflammatory phenotype. 657 hepatocellular adenomas developed in 504 patients were analysed for gene expression of 17 genes and for mutations in seven genes by sequencing. 22 non-mutated IHCAs were analysed by whole-exome and/or RNA sequencing. We identified 296 IHCA (45%), 81% of them were mutated in either Recurrent chromosomal alterations involving

Sections du résumé

BACKGROUND
Inflammatory hepatocellular adenomas (IHCAs) are benign liver tumours characterised by an activation of the janus kinase (JAK)/signal transducers and activators of transcription (STAT) pathway caused by oncogenic activating mutations. However, a subset of IHCA lacks of identified mutation explaining the inflammatory phenotype.
METHODS
657 hepatocellular adenomas developed in 504 patients were analysed for gene expression of 17 genes and for mutations in seven genes by sequencing. 22 non-mutated IHCAs were analysed by whole-exome and/or RNA sequencing.
RESULTS
We identified 296 IHCA (45%), 81% of them were mutated in either
CONCLUSION
Recurrent chromosomal alterations involving

Identifiants

pubmed: 31907296
pii: gutjnl-2019-319790
doi: 10.1136/gutjnl-2019-319790
doi:

Substances chimiques

IL6ST protein, human 0
Neoplasm Proteins 0
Proto-Oncogene Proteins 0
STAT Transcription Factors 0
Cytokine Receptor gp130 133483-10-0
Protein-Tyrosine Kinases EC 2.7.10.1
ROS1 protein, human EC 2.7.10.1
FRK protein, human EC 2.7.10.2
Janus Kinases EC 2.7.10.2

Types de publication

Journal Article Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

1667-1676

Informations de copyright

© Author(s) (or their employer(s)) 2020. No commercial re-use. See rights and permissions. Published by BMJ.

Déclaration de conflit d'intérêts

Competing interests: None declared.

Auteurs

Quentin Bayard (Q)

Centre de Recherche des Cordeliers, Sorbonne Université, Inserm,Université de Paris, Université Paris 13, Functional Genomics of Solid Tumors laboratory, F-75006 Paris, France.

Stefano Caruso (S)

Centre de Recherche des Cordeliers, Sorbonne Université, Inserm,Université de Paris, Université Paris 13, Functional Genomics of Solid Tumors laboratory, F-75006 Paris, France.

Gabrielle Couchy (G)

Centre de Recherche des Cordeliers, Sorbonne Université, Inserm,Université de Paris, Université Paris 13, Functional Genomics of Solid Tumors laboratory, F-75006 Paris, France.

Sandra Rebouissou (S)

Centre de Recherche des Cordeliers, Sorbonne Université, Inserm,Université de Paris, Université Paris 13, Functional Genomics of Solid Tumors laboratory, F-75006 Paris, France.

Paulette Bioulac Sage (P)

Service de Pathologie, Hôpital Pellegrin, CHU de Bordeaux, F 33076 Bordeaux, France.
Université Bordeaux, UMR1053 Bordeaux Research in Translational Oncology, BaRITOn, F-33076 Bordeaux, France.

Charles Balabaud (C)

Université Bordeaux, UMR1053 Bordeaux Research in Translational Oncology, BaRITOn, F-33076 Bordeaux, France.

Valerie Paradis (V)

Service d'anatomopathologie, Hôpital Beaujon, Assistance-Publique Hôpitaux de Paris, Clichy, France.
INSERM U1149, Clichy, France.

Nathalie Sturm (N)

Service d'anatomopathologie, CHU, Grenoble, France.

Anne de Muret (A)

Service d'anatomopathologie, CHU, Tours, France.

Catherine Guettier (C)

Service d'anatomopathologie, CHU Bicètre, Assistance-Publique Hôpitaux de Paris, Bicètre, France, Bicètre, France.

Benjamin Bonsang (B)

Service d'anatomopathologie, Hôpital Henri Mondor; Université Paris Est, Inserm U955, Team 18, Institut Mondor de Recherche Biomédicale, France, Créteil, France.

Christiane Copie (C)

Service d'anatomopathologie, Hôpital Henri Mondor; Université Paris Est, Inserm U955, Team 18, Institut Mondor de Recherche Biomédicale, France, Créteil, France.

Eric Letouzé (E)

Centre de Recherche des Cordeliers, Sorbonne Université, Inserm,Université de Paris, Université Paris 13, Functional Genomics of Solid Tumors laboratory, F-75006 Paris, France.

Julien Calderaro (J)

Service d'anatomopathologie, Hôpital Henri Mondor; Université Paris Est, Inserm U955, Team 18, Institut Mondor de Recherche Biomédicale, France, Créteil, France.

Sandrine Imbeaud (S)

Centre de Recherche des Cordeliers, Sorbonne Université, Inserm,Université de Paris, Université Paris 13, Functional Genomics of Solid Tumors laboratory, F-75006 Paris, France.

Jean-Charles Nault (JC)

Centre de Recherche des Cordeliers, Sorbonne Université, Inserm,Université de Paris, Université Paris 13, Functional Genomics of Solid Tumors laboratory, F-75006 Paris, France naultjc@gmail.com jessica.zucman-rossi@inserm.fr.
Service d'hépatologie, Hôpital Jean Verdier, Hôpitaux Universitaires Paris-Seine-Saint-Denis, Assistance-Publique Hôpitaux de Paris, Bondy, France.
Unité de Formation et de Recherche Santé Médecine et Biologie Humaine, Université Paris 13, Communauté d'Universités et Etablissements Sorbonne Paris Cité, Paris, France, Paris, France.

Jessica Zucman-Rossi (J)

Centre de Recherche des Cordeliers, Sorbonne Université, Inserm,Université de Paris, Université Paris 13, Functional Genomics of Solid Tumors laboratory, F-75006 Paris, France naultjc@gmail.com jessica.zucman-rossi@inserm.fr.
Hôpital Européen Georges Pompidou, F-75015, Assistance Publique-Hôpitaux de Paris, Paris, France.

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Classifications MeSH