SUMO pathway inhibition targets an aggressive pancreatic cancer subtype.


Journal

Gut
ISSN: 1468-3288
Titre abrégé: Gut
Pays: England
ID NLM: 2985108R

Informations de publication

Date de publication:
08 2020
Historique:
received: 02 11 2018
revised: 20 12 2019
accepted: 22 12 2019
pubmed: 1 2 2020
medline: 1 4 2021
entrez: 1 2 2020
Statut: ppublish

Résumé

Pancreatic ductal adenocarcinoma (PDAC) still carries a dismal prognosis with an overall 5-year survival rate of 9%. Conventional combination chemotherapies are a clear advance in the treatment of PDAC; however, subtypes of the disease exist, which exhibit extensive resistance to such therapies. Genomic MYC amplifications represent a distinct subset of PDAC with an aggressive tumour biology. It is clear that hyperactivation of MYC generates dependencies that can be exploited therapeutically. The aim of the study was to find and to target MYC-associated dependencies. We analysed human PDAC gene expression datasets. Results were corroborated by the analysis of the small ubiquitin-like modifier (SUMO) pathway in a large PDAC cohort using immunohistochemistry. A SUMO inhibitor was used and characterised using human and murine two-dimensional, organoid and in vivo models of PDAC. We observed that MYC is connected to the SUMOylation machinery in PDAC. Components of the SUMO pathway characterise a PDAC subtype with a dismal prognosis and we provide evidence that hyperactivation of MYC is connected to an increased sensitivity to pharmacological SUMO inhibition. SUMO inhibitor-based therapies should be further developed for an aggressive PDAC subtype.

Identifiants

pubmed: 32001555
pii: gutjnl-2018-317856
doi: 10.1136/gutjnl-2018-317856
pmc: PMC7398468
doi:

Substances chimiques

Enzyme Inhibitors 0
Esters 0
ML-792 0
MYC protein, human 0
Myc protein, mouse 0
Proto-Oncogene Proteins c-myc 0
Pyrazoles 0
Pyrimidines 0
SUMO-1 Protein 0
SUMO1 protein, human 0
SUMO2 protein, human 0
SUMO3 protein, human 0
Small Ubiquitin-Related Modifier Proteins 0
Sulfonic Acids 0
Ubiquitins 0
Ubiquitin-Conjugating Enzymes EC 2.3.2.23
SAE1 protein, human EC 6.2.1.45
Ubiquitin-Activating Enzymes EC 6.2.1.45
ubiquitin-conjugating enzyme UBC9 EC 6.3.2.-

Types de publication

Journal Article Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

1472-1482

Informations de copyright

© Author(s) (or their employer(s)) 2020. Re-use permitted under CC BY-NC. No commercial re-use. See rights and permissions. Published by BMJ.

Déclaration de conflit d'intérêts

Competing interests: SL is an employee of Takeda Pharmaceutical Company.

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Auteurs

Alexander Biederstädt (A)

Medical Clinic and Policlinic III, Klinikum rechts der Isar, Technical University Munich, München, Germany.

Zonera Hassan (Z)

Medical Clinic and Polyclinic II, Klinikum rechts der Isar, Technical University Munich, München, Germany.

Christian Schneeweis (C)

Medical Clinic and Polyclinic II, Klinikum rechts der Isar, Technical University Munich, München, Germany.

Markus Schick (M)

Department of Hematology, Oncology and Tumor Immunology, Campus Benjamin Franklin, Charité - Universitätsmedizin Berlin, Berlin, Germany.

Lara Schneider (L)

Center for Bioinformatics, Saarland Informatics Campus, Saarland University, Saarbrücken, Germany.
Saarbrücken Graduate School of Computer Science, Saarland Informatics Campus, Saarland University, Saarbrücken, Germany.

Alexander Muckenhuber (A)

Institute of Pathology, Technical University Munich, München, Germany.

Yingfen Hong (Y)

Medical Clinic and Policlinic III, Klinikum rechts der Isar, Technical University Munich, München, Germany.

Gerrit Siegers (G)

Medical Clinic and Policlinic III, Klinikum rechts der Isar, Technical University Munich, München, Germany.

Lisa Nilsson (L)

Department of Surgery, Sahlgrenska Cancer Center, Gothenburg University, Gothenburg, Sweden.

Matthias Wirth (M)

Department of Hematology, Oncology and Tumor Immunology, Campus Benjamin Franklin, Charité - Universitätsmedizin Berlin, Berlin, Germany.

Zahra Dantes (Z)

Medical Clinic and Polyclinic II, Klinikum rechts der Isar, Technical University Munich, München, Germany.

Katja Steiger (K)

Institute of Pathology, Technical University Munich, München, Germany.
German Cancer Research Center (DKFZ) and German Cancer Consortium (DKTK), Heidelberg, Germany.

Kathrin Schunck (K)

Goethe University, Medical School, Institute of Biochemistry II, Frankfurt, Germany.

Steve Langston (S)

Oncology Drug Discovery Unit, Takeda Pharmaceuticals International Co, Cambridge, Massachusetts, USA.

H-P Lenhof (HP)

Center for Bioinformatics, Saarland Informatics Campus, Saarland University, Saarbrücken, Germany.

Andrea Coluccio (A)

Medical Clinic and Polyclinic II, Klinikum rechts der Isar, Technical University Munich, München, Germany.
Institute for Translational Cancer Research and Experimental Cancer Therapy, Technical University Munich, München, Germany.

Felix Orben (F)

Medical Clinic and Polyclinic II, Klinikum rechts der Isar, Technical University Munich, München, Germany.

Jolanta Slawska (J)

Medical Clinic and Policlinic III, Klinikum rechts der Isar, Technical University Munich, München, Germany.

Anna Scherger (A)

Medical Clinic and Policlinic III, Klinikum rechts der Isar, Technical University Munich, München, Germany.

Dieter Saur (D)

German Cancer Research Center (DKFZ) and German Cancer Consortium (DKTK), Heidelberg, Germany.
Institute for Translational Cancer Research and Experimental Cancer Therapy, Technical University Munich, München, Germany.

Stefan Müller (S)

Goethe University, Medical School, Institute of Biochemistry II, Frankfurt, Germany.

Roland Rad (R)

German Cancer Research Center (DKFZ) and German Cancer Consortium (DKTK), Heidelberg, Germany.
Institute of Molecular Oncology and Functional Genomics, Technical University Munich, München, Germany.

Wilko Weichert (W)

Institute of Pathology, Technical University Munich, München, Germany.
German Cancer Research Center (DKFZ) and German Cancer Consortium (DKTK), Heidelberg, Germany.

Jonas Nilsson (J)

Department of Surgery, Sahlgrenska Cancer Center, Gothenburg University, Gothenburg, Sweden.

Maximilian Reichert (M)

Medical Clinic and Polyclinic II, Klinikum rechts der Isar, Technical University Munich, München, Germany.
German Cancer Research Center (DKFZ) and German Cancer Consortium (DKTK), Heidelberg, Germany.

Günter Schneider (G)

Medical Clinic and Polyclinic II, Klinikum rechts der Isar, Technical University Munich, München, Germany guenter.schneider@tum.de ulrich.keller@charite.de.
German Cancer Research Center (DKFZ) and German Cancer Consortium (DKTK), Heidelberg, Germany.

Ulrich Keller (U)

Department of Hematology, Oncology and Tumor Immunology, Campus Benjamin Franklin, Charité - Universitätsmedizin Berlin, Berlin, Germany guenter.schneider@tum.de ulrich.keller@charite.de.
German Cancer Research Center (DKFZ) and German Cancer Consortium (DKTK), Heidelberg, Germany.

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