Safety and Utility of Cardiopulmonary Exercise Testing in Arrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia.
Adolescent
Adult
Arrhythmogenic Right Ventricular Dysplasia
/ diagnosis
Exercise Test
/ adverse effects
Exercise Tolerance
Female
Heart Failure
/ diagnosis
Heart Transplantation
Humans
Male
Middle Aged
Oxygen Consumption
Predictive Value of Tests
Progression-Free Survival
Registries
Retrospective Studies
Risk Assessment
Risk Factors
Young Adult
arrhythmias
cardiomyopathy
exercise testing
genetics
heart failure
transplantation
Journal
Journal of the American Heart Association
ISSN: 2047-9980
Titre abrégé: J Am Heart Assoc
Pays: England
ID NLM: 101580524
Informations de publication
Date de publication:
04 02 2020
04 02 2020
Historique:
entrez:
4
2
2020
pubmed:
6
2
2020
medline:
15
12
2020
Statut:
ppublish
Résumé
Background Arrhythmogenic right ventricular cardiomyopathy/dysplasia (ARVC/D) is characterized by high arrhythmic burden and progressive heart failure, which can prompt referral for heart transplantation. Cardiopulmonary exercise testing (CPET) has an established role in risk stratification for advanced heart failure therapies, but has not been described in ARVC/D. This study sought to determine the safety and prognostic utility of CPET in patients with ARVC/D. Methods and Results Using the Johns Hopkins ARVC/D Registry, we examined patients with ARVC/D undergoing CPET. Baseline characteristics and transplant-free survival were compared on the basis of peak oxygen consumption (pVO2) (≤14 or >14 mL/kg per minute) and ventilatory efficiency (Ve/VCO
Identifiants
pubmed: 32009524
doi: 10.1161/JAHA.119.013695
pmc: PMC7033873
doi:
Types de publication
Journal Article
Observational Study
Research Support, Non-U.S. Gov't
Langues
eng
Sous-ensembles de citation
IM
Pagination
e013695Commentaires et corrections
Type : CommentIn
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