Ebstein Anomaly in the Adult Patient.
Accessory pathway
Cone repair
Ebstein anomaly
Pregnancy
Tricuspid valve
Journal
Cardiology clinics
ISSN: 1558-2264
Titre abrégé: Cardiol Clin
Pays: Netherlands
ID NLM: 8300331
Informations de publication
Date de publication:
Aug 2020
Aug 2020
Historique:
entrez:
6
7
2020
pubmed:
6
7
2020
medline:
27
4
2021
Statut:
ppublish
Résumé
Ebstein anomaly is a congenital malformation involving primarily the tricuspid valve, with failure of delamination from the underlying myocardium and right ventricular myopathy. Echocardiography is diagnostic in most patients and demonstrates apical displacement of the septal leaflet and variable tethering of leaflet tissue to the right ventricular myocardium. Operative intervention is considered for exertional symptoms, progressive right ventricular enlargement, or right ventricular dysfunction. Tricuspid valve cone repair is the preferred surgical approach. Tricuspid valve replacement and bidirectional cavopulmonary shunt also are considered in patients with advanced disease. Pregnancy generally is well tolerated. Patients with Ebstein anomaly require lifelong follow-up.
Identifiants
pubmed: 32622490
pii: S0733-8651(20)30027-8
doi: 10.1016/j.ccl.2020.04.004
pii:
doi:
Types de publication
Journal Article
Review
Langues
eng
Sous-ensembles de citation
IM
Pagination
353-363Informations de copyright
Copyright © 2020 Elsevier Inc. All rights reserved.
Déclaration de conflit d'intérêts
Disclosure The authors have nothing to disclose.