A Possible Role for Arylsulfatase G in Dermatan Sulfate Metabolism.
Amino Acid Sequence
Arylsulfatases
/ biosynthesis
Catalytic Domain
Dermatan Sulfate
/ metabolism
Endothelial Cells
/ drug effects
Gene Silencing
Humans
Models, Molecular
Mucopolysaccharidosis VI
/ metabolism
Myocytes, Smooth Muscle
/ drug effects
N-Acetylgalactosamine-4-Sulfatase
/ chemistry
Organ Specificity
Protein Binding
Protein Conformation
Pulmonary Artery
/ cytology
RNA, Messenger
/ biosynthesis
Sequence Alignment
Sequence Homology, Amino Acid
Tissue Array Analysis
Up-Regulation
arylsulfatase
dermatan sulfate
mucopolysaccharidosis
smooth muscle cell
Journal
International journal of molecular sciences
ISSN: 1422-0067
Titre abrégé: Int J Mol Sci
Pays: Switzerland
ID NLM: 101092791
Informations de publication
Date de publication:
12 Jul 2020
12 Jul 2020
Historique:
received:
02
06
2020
revised:
01
07
2020
accepted:
06
07
2020
entrez:
16
7
2020
pubmed:
16
7
2020
medline:
27
2
2021
Statut:
epublish
Résumé
Perturbations of glycosaminoglycan metabolism lead to mucopolysaccharidoses (MPS)-lysosomal storage diseases. One type of MPS (type VI) is associated with a deficiency of arylsulfatase B (ARSB), for which we previously established a cellular model using pulmonary artery endothelial cells with a silenced
Identifiants
pubmed: 32664626
pii: ijms21144913
doi: 10.3390/ijms21144913
pmc: PMC7404199
pii:
doi:
Substances chimiques
RNA, Messenger
0
Dermatan Sulfate
24967-94-0
ARSG protein, human
EC 3.1.6.-
Arylsulfatases
EC 3.1.6.1
N-Acetylgalactosamine-4-Sulfatase
EC 3.1.6.12
ARSB protein, human
EC 3.1.6.12.
Types de publication
Comparative Study
Journal Article
Langues
eng
Sous-ensembles de citation
IM
Subventions
Organisme : Polish Cardiac Society
ID : 2012 annual prize and scientific grant of the Polish Cardiac Society
Organisme : Narodowe Centrum Nauki
ID : DEC-2016/21/B/ST7/02241
Organisme : Narodowe Centrum Nauki
ID : 2015/19/D/NZ1/03443
Références
J Tissue Eng Regen Med. 2017 May;11(5):1365-1376
pubmed: 26033955
Carbohydr Res. 2012 Jul 15;356:233-7
pubmed: 22533918
PLoS One. 2013 Nov 22;8(11):e82456
pubmed: 24278482
J Biol Chem. 1998 Mar 13;273(11):6096-103
pubmed: 9497327
J Chem Theory Comput. 2015 Jul 14;11(7):3499-509
pubmed: 26190950
Biomacromolecules. 2014 Jun 9;15(6):2090-103
pubmed: 24806357
Front Biosci (Landmark Ed). 2017 Jan 1;22:385-406
pubmed: 27814620
Genome Biol. 2004;5(10):R80
pubmed: 15461798
Mol Vis. 2009;15:482-94
pubmed: 19262745
Mol Genet Metab Rep. 2015 Feb 28;3:11-7
pubmed: 26937388
Methods Enzymol. 2005;400:273-93
pubmed: 16399355
Biochem Res Int. 2012;2012:471325
pubmed: 22013531
Orphanet J Rare Dis. 2010 Apr 12;5:5
pubmed: 20385007
Hum Mutat. 2007 Sep;28(9):897-903
pubmed: 17458871
Eur J Biochem. 1996 Jun 1;238(2):341-5
pubmed: 8681943
J Biol Chem. 2004 Nov 19;279(47):48640-6
pubmed: 15347686
Curr Opin Genet Dev. 1997 Jun;7(3):386-91
pubmed: 9229115
J Biol Chem. 2008 Apr 25;283(17):11388-95
pubmed: 18283100
J Biol Chem. 2002 Nov 8;277(45):42815-20
pubmed: 12215437
J Biol Chem. 2014 Oct 3;289(40):27992-8005
pubmed: 25135642
J Biol Chem. 1998 Oct 23;273(43):28116-21
pubmed: 9774430
Methods. 2001 Dec;25(4):402-8
pubmed: 11846609
Acta Biomater. 2014 Apr;10(4):1705-19
pubmed: 24121191
Vasc Cell. 2015 Sep 18;7:8
pubmed: 26388991
Bioinformatics. 2003 Jan 22;19(2):185-93
pubmed: 12538238
Cell Mol Life Sci. 2007 Aug;64(15):2013-22
pubmed: 17558559
Clin Chim Acta. 2011 May 12;412(11-12):906-13
pubmed: 21256835
Eur J Hum Genet. 2002 Dec;10(12):813-8
pubmed: 12461688
ACS Chem Biol. 2015 Jan 16;10(1):72-84
pubmed: 25514000