Management challenges of a large upper extremity vascular malformation in a patient with capillary malformation-arteriovenous malformation syndrome.
Adolescent
Arm
/ blood supply
Arteriovenous Malformations
/ complications
Blood Transfusion
Capillaries
/ abnormalities
Disarticulation
Embolization, Therapeutic
Hemorrhage
/ etiology
Hemostatic Techniques
Humans
Male
Myocutaneous Flap
Port-Wine Stain
/ complications
Recurrence
Shoulder
/ blood supply
Thoracic Wall
/ blood supply
Treatment Outcome
Vascular Surgical Procedures
Arteriovenous malformation
CM-AVM syndrome
Embolization
Pediatric
Journal
Journal of vascular surgery. Venous and lymphatic disorders
ISSN: 2213-3348
Titre abrégé: J Vasc Surg Venous Lymphat Disord
Pays: United States
ID NLM: 101607771
Informations de publication
Date de publication:
05 2021
05 2021
Historique:
received:
27
04
2020
accepted:
07
07
2020
pubmed:
21
7
2020
medline:
29
6
2021
entrez:
21
7
2020
Statut:
ppublish
Résumé
We describe a 17-year-old boy with capillary malformation-arteriovenous malformation syndrome and a massive vascular malformation of the right chest wall, shoulder, and upper arm. Persistent growth of the malformation caused cutaneous ulcerations and recurrent massive bleeding episodes. We proceeded with a modified shoulder disarticulation preceded by ligation of the subclavian artery and innominate vein by median sternotomy. After a staged debulking resection of the residual chest wall arteriovenous malformation with rotational transverse rectus abdominis myocutaneous flap coverage, the patient was discharged home safely. This report demonstrates that a multidisciplinary approach is critical for management of life-threatening complications in capillary malformation-arteriovenous malformation patients.
Identifiants
pubmed: 32687897
pii: S2213-333X(20)30406-6
doi: 10.1016/j.jvsv.2020.07.001
pii:
doi:
Types de publication
Case Reports
Langues
eng
Sous-ensembles de citation
IM
Pagination
781-784Informations de copyright
Copyright © 2020 Society for Vascular Surgery. Published by Elsevier Inc. All rights reserved.