Congenitally corrected transposition and mitral atresia complicated by restrictive atrial septum.
Ebstein anomaly
ccTGA
fetal echocardiography
mitral atresia
pediatric cardiology
Journal
Journal of clinical ultrasound : JCU
ISSN: 1097-0096
Titre abrégé: J Clin Ultrasound
Pays: United States
ID NLM: 0401663
Informations de publication
Date de publication:
Oct 2020
Oct 2020
Historique:
received:
15
05
2019
revised:
26
05
2020
accepted:
04
07
2020
pubmed:
5
8
2020
medline:
25
2
2021
entrez:
5
8
2020
Statut:
ppublish
Résumé
Congenitally corrected transposition (ccTGA), also known as L-transposition of the great arteries (L-TGA), is a rare cardiac malformation accounting for approximately 0.05% of congenital heart disease, characterized by ventricular inversion, discordant ventriculo-arterial connections with a normal visceroatrial relationship. It was first described by Baron Rokitansky in 1875, and prenatal sonographic diagnosis can be difficult. Symptomatology and clinical presentation of this malformation are related to the associated intracardiac defects. We report a rare case of severe, complex cardiac disease: prenatally diagnosed ccTGA with atrial restriction, mitral atresia, Ebsteinoid tricuspid valve, and severe pulmonary valve stenosis, who subsequently developed left pulmonary vein stenosis.
Types de publication
Case Reports
Langues
eng
Sous-ensembles de citation
IM
Pagination
510-512Informations de copyright
© 2020 Wiley Periodicals LLC.
Références
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