Premature Onset Aortic Stenosis in Systemic Sclerosis: A Report of a Series of Cases.


Journal

Internal medicine (Tokyo, Japan)
ISSN: 1349-7235
Titre abrégé: Intern Med
Pays: Japan
ID NLM: 9204241

Informations de publication

Date de publication:
15 Dec 2020
Historique:
pubmed: 14 8 2020
medline: 15 4 2021
entrez: 14 8 2020
Statut: ppublish

Résumé

Although cardiovascular involvement is a well-known complication correlated with a poor prognosis in patients with systemic sclerosis, there are few reports on valvular heart disease. Forty patients with systemic sclerosis were retrospectively analyzed. Valvular heart disease was found in six patients, five of whom had severe tri-leaflet aortic stenosis. Three of these 5 patients were ≤71 years old. Two frail elderly patients who underwent transcatheter aortic valve replacement died within two years. Premature-onset aortic stenosis is not uncommon in patients with systemic sclerosis. When considering mechanical intervention, the evaluation of frailty is important.

Identifiants

pubmed: 32788545
doi: 10.2169/internalmedicine.5226-20
pmc: PMC7807118
doi:

Types de publication

Journal Article

Langues

eng

Sous-ensembles de citation

IM

Pagination

3177-3181

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Auteurs

Ayaka Machida (A)

Department of Medicine, Chikamori Hospital, Japan.

Takashi Funaki (T)

Department of Medicine, Chikamori Hospital, Japan.
Department of Cardiology and Aging Science, Kochi Medical School, Japan.

Koji Nishida (K)

Department of Medicine, Chikamori Hospital, Japan.

Ryu-Ichiro Imai (RI)

Department of Medicine, Chikamori Hospital, Japan.

Yoko Nakaoka (Y)

Department of Medicine, Chikamori Hospital, Japan.

Shu-Ichi Seki (SI)

Department of Medicine, Chikamori Hospital, Japan.

Yu-Ichi Baba (YI)

Department of Cardiology and Aging Science, Kochi Medical School, Japan.

Toru Kubo (T)

Department of Cardiology and Aging Science, Kochi Medical School, Japan.

Naohito Yamasaki (N)

Department of Cardiology and Aging Science, Kochi Medical School, Japan.

Hiroaki Kitaoka (H)

Department of Cardiology and Aging Science, Kochi Medical School, Japan.

Sho-Ichi Kubokawa (SI)

Department of Medicine, Chikamori Hospital, Japan.

Hiroshi Sakaeda (H)

Department of Medicine, Chikamori Hospital, Japan.

Kazuya Kawai (K)

Department of Medicine, Chikamori Hospital, Japan.

Naohisa Hamashige (N)

Department of Medicine, Chikamori Hospital, Japan.

Yoshinori Doi (Y)

Department of Medicine, Chikamori Hospital, Japan.
Cardiomyopathy Institute, Chikamori Hospital, Japan.

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