Founder Mutation in N Terminus of Cardiac Troponin I Causes Malignant Hypertrophic Cardiomyopathy.


Journal

Circulation. Genomic and precision medicine
ISSN: 2574-8300
Titre abrégé: Circ Genom Precis Med
Pays: United States
ID NLM: 101714113

Informations de publication

Date de publication:
10 2020
Historique:
pubmed: 5 9 2020
medline: 28 10 2021
entrez: 5 9 2020
Statut: ppublish

Résumé

Cardiac troponin I ( We sequenced 29 families with hypertrophic cardiomyopathy enriched for pediatric-onset disease and identified 5 families with the All 5 families with The

Sections du résumé

BACKGROUND
Cardiac troponin I (
METHODS
We sequenced 29 families with hypertrophic cardiomyopathy enriched for pediatric-onset disease and identified 5 families with the
RESULTS
All 5 families with
CONCLUSIONS
The

Identifiants

pubmed: 32885985
doi: 10.1161/CIRCGEN.120.002991
pmc: PMC7676616
doi:

Substances chimiques

Troponin I 0

Types de publication

Journal Article Research Support, N.I.H., Extramural Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

444-452

Subventions

Organisme : Wellcome Trust
ID : 107469
Pays : United Kingdom
Organisme : Howard Hughes Medical Institute
Pays : United States
Organisme : Medical Research Council
ID : MC_UP_1102/20
Pays : United Kingdom
Organisme : NIGMS NIH HHS
ID : T32 GM007753
Pays : United States
Organisme : Wellcome Trust
ID : 107469/Z/15/Z
Pays : United Kingdom

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Auteurs

Akl C Fahed (AC)

Division of Cardiology, Department of Medicine, Center of Genomic Medicine, Massachusetts General Hospital (A.C.F.), Harvard Medical School, Boston.
Cardiovascular Disease Initiative, Broad Institute of MIT and Harvard, Cambridge, MA (A.C.F.).

Georges Nemer (G)

Department of Biochemistry and Molecular Genetics, American University of Beirut, Lebanon (G.N., F.F.B., M.B., A.K., O.A.-H.).
College of Health and Life Sciences, Hamad Bin Khalifa University, Education City, Doha, Qatar (G.N.).

Fadi F Bitar (FF)

Department of Biochemistry and Molecular Genetics, American University of Beirut, Lebanon (G.N., F.F.B., M.B., A.K., O.A.-H.).
Department of Pediatrics (F.F.B., M.T.A.), American University of Beirut Medical Center, Lebanon.

Samir Arnaout (S)

Cardiology Division (S.A., A.B.A., O.A.-H.), American University of Beirut Medical Center, Lebanon.

Antoine B Abchee (AB)

Cardiology Division (S.A., A.B.A., O.A.-H.), American University of Beirut Medical Center, Lebanon.

Manal Batrawi (M)

Department of Biochemistry and Molecular Genetics, American University of Beirut, Lebanon (G.N., F.F.B., M.B., A.K., O.A.-H.).

Athar Khalil (A)

Department of Biochemistry and Molecular Genetics, American University of Beirut, Lebanon (G.N., F.F.B., M.B., A.K., O.A.-H.).

Ossama K Abou Hassan (OK)

Department of Biochemistry and Molecular Genetics, American University of Beirut, Lebanon (G.N., F.F.B., M.B., A.K., O.A.-H.).
Cardiology Division (S.A., A.B.A., O.A.-H.), American University of Beirut Medical Center, Lebanon.

Steven R DePalma (SR)

Department of Genetics (S.R.D., B.M., J.G.S., C.E.S.), Harvard Medical School, Boston.

Barbara McDonough (B)

Department of Genetics (S.R.D., B.M., J.G.S., C.E.S.), Harvard Medical School, Boston.

Mariam T Arabi (MT)

Department of Pediatrics (F.F.B., M.T.A.), American University of Beirut Medical Center, Lebanon.

James S Ware (JS)

National Heart and Lung Institute, Imperial College London, Royal Brompton Hospital (J.S.W.).
Medical Research College London Institute of Medical Sciences, United Kingdom (J.S.W.).

Jonathan G Seidman (JG)

Department of Genetics (S.R.D., B.M., J.G.S., C.E.S.), Harvard Medical School, Boston.

Christine E Seidman (CE)

Department of Genetics (S.R.D., B.M., J.G.S., C.E.S.), Harvard Medical School, Boston.
Division of Cardiology and Howard Hughes Medical Institute, Brigham and Women's Hospital, Boston, MA (C.E.S.).

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