AQP4 autoantibodies in patients with idiopathic normal pressure hydrocephalus.


Journal

Journal of neuroimmunology
ISSN: 1872-8421
Titre abrégé: J Neuroimmunol
Pays: Netherlands
ID NLM: 8109498

Informations de publication

Date de publication:
15 12 2020
Historique:
received: 04 08 2020
revised: 14 09 2020
accepted: 24 09 2020
pubmed: 9 10 2020
medline: 17 12 2020
entrez: 8 10 2020
Statut: ppublish

Résumé

Idiopathic normal pressure hydrocephalus (iNPH) is a common neurological disorder with unknown etiology. A selective depletion of aquaporin 4 (AQP4) has been shown in iNPH patients. We collected serum and cerebrospinal fluid (CSF) from 43 iNPH patients and 35 with other neurodegenerative conditions, and serum from 43 healthy subjects. All samples were tested for AQP4-IgG/IgA/IgM antibodies using a live cell-based assay. No patients or controls had serum/CSF AQP4-IgG/IgA. One/43 iNPH patient and 0/43 controls tested positive for serum AQP4-IgM. The AQP4-IgM-positive iNPH patient had no clinico-radiological distinctive features. AQP4 antibodies are unlikely to play a role in iNPH pathogenesis.

Identifiants

pubmed: 33032017
pii: S0165-5728(20)30526-9
doi: 10.1016/j.jneuroim.2020.577407
pii:
doi:

Substances chimiques

AQP4 protein, human 0
Aquaporin 4 0
Autoantibodies 0
Biomarkers 0

Types de publication

Journal Article Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

577407

Informations de copyright

Copyright © 2020 Elsevier B.V. All rights reserved.

Auteurs

Matteo Gastaldi (M)

Neuroimmunology Laboratory, IRCCS Mondino Foundation, Pavia, Italy; Neuro-oncology and Neuroinflammation Unit, IRCCS Mondino Foundation, Pavia, Italy. Electronic address: matteo.gastaldi@mondino.it.

Massimiliano Todisco (M)

Parkinson's Disease and Movement Disorders Unit, IRCCS Mondino Foundation, Pavia, Italy; Department of Brain and Behavioral Sciences, University of Pavia, Pavia, Italy.

Giorgia Carlin (G)

Neuroimmunology Laboratory, IRCCS Mondino Foundation, Pavia, Italy.

Silvia Scaranzin (S)

Neuroimmunology Laboratory, IRCCS Mondino Foundation, Pavia, Italy. Electronic address: silvia.scaranzin@gmail.com.

Elisabetta Zardini (E)

Neuroimmunology Laboratory, IRCCS Mondino Foundation, Pavia, Italy. Electronic address: zardini@unipv.it.

Brigida Minafra (B)

Parkinson's Disease and Movement Disorders Unit, IRCCS Mondino Foundation, Pavia, Italy.

Roberta Zangaglia (R)

Parkinson's Disease and Movement Disorders Unit, IRCCS Mondino Foundation, Pavia, Italy.

Anna Pichiecchio (A)

Neuroradiology Department, IRCCS Mondino Foundation, Pavia, Italy. Electronic address: anna.pichiecchio@mondino.it.

Markus Reindl (M)

Clinical Department of Neurology, Medical University of Innsbruck, Innsbruck, Austria.

Sven Jarius (S)

Molecular Neuroimmunology Group, Department of Neurology, University of Heidelberg, Otto Meyerhof Center, Heidelberg, Germany.

Claudio Pacchetti (C)

Parkinson's Disease and Movement Disorders Unit, IRCCS Mondino Foundation, Pavia, Italy.

Diego Franciotta (D)

Neuroimmunology Laboratory, IRCCS Mondino Foundation, Pavia, Italy.

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Classifications MeSH