Bullous Pemphigoid: Trigger and Predisposing Factors.


Journal

Biomolecules
ISSN: 2218-273X
Titre abrégé: Biomolecules
Pays: Switzerland
ID NLM: 101596414

Informations de publication

Date de publication:
10 10 2020
Historique:
received: 07 09 2020
revised: 01 10 2020
accepted: 08 10 2020
entrez: 14 10 2020
pubmed: 15 10 2020
medline: 8 9 2021
Statut: epublish

Résumé

Bullous pemphigoid (BP) is the most frequent autoimmune subepidermal blistering disease provoked by autoantibodies directed against two hemidesmosomal proteins: BP180 and BP230. Its pathogenesis depends on the interaction between predisposing factors, such as human leukocyte antigen (HLA) genes, comorbidities, aging, and trigger factors. Several trigger factors, such as drugs, thermal or electrical burns, surgical procedures, trauma, ultraviolet irradiation, radiotherapy, chemical preparations, transplants, and infections may induce or exacerbate BP disease. Identification of predisposing and trigger factors can increase the understanding of BP pathogenesis. Furthermore, an accurate anamnesis focused on the recognition of a possible trigger factor can improve prognosis by promptly removing it.

Identifiants

pubmed: 33050407
pii: biom10101432
doi: 10.3390/biom10101432
pmc: PMC7600534
pii:
doi:

Substances chimiques

HLA Antigens 0

Types de publication

Journal Article Research Support, Non-U.S. Gov't Review

Langues

eng

Sous-ensembles de citation

IM

Subventions

Organisme : Italian Ministry of Health, Rome, Italy
ID : "Progetto Ricerca Corrente - 2019" and "Ricerca Finalizzata-2020"

Déclaration de conflit d'intérêts

The authors declare no conflicts of interest.

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Auteurs

Jo Linda Maria Sinagra (JLM)

IDI-IRCCS, via dei Monti di Creta 104, 00167 Rome, Italy.

Adele Salemme (A)

IDI-IRCCS, via dei Monti di Creta 104, 00167 Rome, Italy.

Giovanni Di Zenzo (G)

IDI-IRCCS, via dei Monti di Creta 104, 00167 Rome, Italy.

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