Challenges in Cardiac and Pulmonary Sarcoidosis: JACC State-of-the-Art Review.
biomarkers
cardiac sarcoidosis
imaging
pulmonary sarcoidosis
Journal
Journal of the American College of Cardiology
ISSN: 1558-3597
Titre abrégé: J Am Coll Cardiol
Pays: United States
ID NLM: 8301365
Informations de publication
Date de publication:
20 10 2020
20 10 2020
Historique:
received:
26
02
2020
revised:
12
08
2020
accepted:
13
08
2020
entrez:
16
10
2020
pubmed:
17
10
2020
medline:
10
2
2021
Statut:
ppublish
Résumé
Sarcoidosis is a complex disease with heterogeneous clinical presentations that can affect virtually any organ. Although the lung is typically the most common organ involved, combined pulmonary and cardiac sarcoidosis (CS) account for most of the morbidity and mortality associated with this disease. Pulmonary sarcoidosis can be asymptomatic or result in impairment in quality of life and end-stage, severe, and/or life-threatening disease. The latter outcome is seen almost exclusively in those with fibrotic pulmonary sarcoidosis, which accounts for 10% to 20% of pulmonary sarcoidosis patients. CS is problematic to diagnose and may cause significant morbidity and death from heart failure or ventricular arrhythmias. The diagnosis of CS usually requires surrogate cardiac imaging biomarkers, as endomyocardial biopsy has relatively low yield, even with directed electrophysiological mapping. Treatment of CS is often multifactorial, involving a combination of antigranulomatous therapy and pharmacotherapy for cardiac arrhythmias and/or heart failure in addition to device placement and cardiac transplantation.
Identifiants
pubmed: 33059834
pii: S0735-1097(20)36410-X
doi: 10.1016/j.jacc.2020.08.042
pmc: PMC7808240
mid: NIHMS1624374
pii:
doi:
Substances chimiques
Antibodies, Monoclonal
0
Types de publication
Journal Article
Research Support, N.I.H., Extramural
Review
Langues
eng
Sous-ensembles de citation
IM
Pagination
1878-1901Subventions
Organisme : NCATS NIH HHS
ID : KL2 TR001435
Pays : United States
Organisme : NHLBI NIH HHS
ID : R01 HL071021
Pays : United States
Organisme : NHLBI NIH HHS
ID : R01 HL117074
Pays : United States
Organisme : NHLBI NIH HHS
ID : R01 HL148167
Pays : United States
Informations de copyright
Copyright © 2020 American College of Cardiology Foundation. Published by Elsevier Inc. All rights reserved.
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