Vanishing White Matter Hyperintensities in CADASIL: A Case Report with Insight into Disease Mechanisms.


Journal

Journal of Alzheimer's disease : JAD
ISSN: 1875-8908
Titre abrégé: J Alzheimers Dis
Pays: Netherlands
ID NLM: 9814863

Informations de publication

Date de publication:
2020
Historique:
pubmed: 20 10 2020
medline: 28 9 2021
entrez: 19 10 2020
Statut: ppublish

Résumé

In a woman with Cerebral Autosomal Dominant Arteriopathy with Subcortical Infarcts and Leukoencephalopathy (CADASIL) followed for 15 years, we observed magnetic resonance imaging white matter hyperintensities that vanished in the anterior temporal poles while the brain volume decreased unexpectedly. These imaging changes were transient and detected when the patient was being treated by valproic acid for stabilizing mood disturbances. This intriguing case supports that mechanisms underlying white matter hyperintensities can vary from one brain area to another and that important modifications of water influx into the brain tissue might be involved in some imaging features of CADASIL.

Identifiants

pubmed: 33074242
pii: JAD201086
doi: 10.3233/JAD-201086
doi:

Substances chimiques

Antimanic Agents 0
Lithium Compounds 0
Valproic Acid 614OI1Z5WI
dipropylacetamide RUA6CWU76G

Types de publication

Case Reports Letter Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

907-910

Auteurs

Eric Jouvent (E)

Université de Paris, Paris, France.
APHP, Lariboisière Hospital, Department of Neurology and Referral Center for rare vascular diseases of the brain and retina (CERVCO), Paris, France.
FHU NeuroVasc, Université de Paris, Paris, France.
U1141 INSERM, Paris, France.

Nassira Alili (N)

APHP, Lariboisière Hospital, Department of Neurology and Referral Center for rare vascular diseases of the brain and retina (CERVCO), Paris, France.
FHU NeuroVasc, Université de Paris, Paris, France.

Dominique Hervé (D)

APHP, Lariboisière Hospital, Department of Neurology and Referral Center for rare vascular diseases of the brain and retina (CERVCO), Paris, France.
FHU NeuroVasc, Université de Paris, Paris, France.

Hugues Chabriat (H)

Université de Paris, Paris, France.
APHP, Lariboisière Hospital, Department of Neurology and Referral Center for rare vascular diseases of the brain and retina (CERVCO), Paris, France.
FHU NeuroVasc, Université de Paris, Paris, France.
U1141 INSERM, Paris, France.

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Classifications MeSH