A case of eosinophilic granulomatosis with polyangiitis as a mimicker of IgG4-related disease.
Bird’s eye pattern
Eosinophilic granulomatosis with polyangiitis
IgG-related disease
IgG4-related kidney disease
Storiform fibrosis
Journal
Modern rheumatology case reports
ISSN: 2472-5625
Titre abrégé: Mod Rheumatol Case Rep
Pays: England
ID NLM: 101761026
Informations de publication
Date de publication:
07 2020
07 2020
Historique:
entrez:
22
10
2020
pubmed:
23
10
2020
medline:
27
8
2021
Statut:
ppublish
Résumé
A 62-year-old woman was admitted to our hospital because of fever, renal dysfunction, eosinophilia, and the presence of MPO-ANCA. Based on the renal pathological examination which showed granuloma lesion with eosinophils and crescentic glomerulonephritis, eosinophilic granulomatosis with polyangiitis (EGPA) was diagnosed. On the other hand, laboratory examination showed elevated serum IgG4 levels and renal pathological examination showed marked lymphoplasmacytic infiltration and fibrosis surrounding nest "Bird's eye pattern," which were characteristic of IgG4-related kidney disease (IgG4-RKD). Because there are cases when EGPA has clinical features of IgG4-RKD, we should be careful about diagnoses of IgG4-RKD in patients with EGPA.
Identifiants
pubmed: 33087011
doi: 10.1080/24725625.2020.1759200
doi:
Substances chimiques
Biomarkers
0
Types de publication
Case Reports
Journal Article
Langues
eng
Sous-ensembles de citation
IM