Cardiac amyloidosis-A review of current literature for the practicing physician.
AL
ATTR
amyloid deposits
amyloidosis
cardiac amyloidosis
Journal
Clinical cardiology
ISSN: 1932-8737
Titre abrégé: Clin Cardiol
Pays: United States
ID NLM: 7903272
Informations de publication
Date de publication:
Mar 2021
Mar 2021
Historique:
received:
22
11
2020
revised:
01
02
2021
accepted:
08
02
2021
pubmed:
18
2
2021
medline:
16
10
2021
entrez:
17
2
2021
Statut:
ppublish
Résumé
The amyloidoses are a family of diseases in which misfolded precursor proteins aggregate to form amyloid and deposit in body tissues. A very serious yet underrecognized form of this disease is cardiac amyloidosis, in which amyloid deposits into the extracellular space of the myocardium, resulting in thickening and stiffening of ventricular walls with resultant heart failure and conductive dysfunction. This review provides a discussion of the pathogenesis and clinical presentation of cardiac amyloidosis subtypes, as well as an up-to-date approach to diagnosis and treatment. Significant progress has been made in recent years regarding diagnosis and treatment of this condition, but prognosis remains heavily reliant on early detection of the disease. Two types of precursor protein are responsible for most cardiac amyloidosis cases: transthyretin amyloid, and immunoglobulin-derived light chain amyloid. An early diagnosis of cardiac amyloidosis can allow for novel treatment modalities to be initiated with the potential to improve prognosis.
Identifiants
pubmed: 33595871
doi: 10.1002/clc.23572
pmc: PMC7943900
doi:
Substances chimiques
Amyloid
0
Immunoglobulin Light Chains
0
Prealbumin
0
Types de publication
Journal Article
Review
Langues
eng
Sous-ensembles de citation
IM
Pagination
322-331Informations de copyright
© 2021 The Authors. Clinical Cardiology published by Wiley Periodicals LLC.
Références
Cardiovasc Pathol. 2015 Nov-Dec;24(6):343-50
pubmed: 26361138
J Am Coll Cardiol. 2016 Sep 20;68(12):1323-41
pubmed: 27634125
Eur Heart J. 2017 Jun 21;38(24):1905-1908
pubmed: 28605421
JAMA. 2013 Dec 25;310(24):2658-67
pubmed: 24368466
Ann Med. 2007;39(3):200-7
pubmed: 17457717
Neurodegener Dis Manag. 2019 Feb;9(1):5-23
pubmed: 30480471
Magn Reson Imaging Clin N Am. 2019 Aug;27(3):453-463
pubmed: 31279449
Br Heart J. 1995 Nov;74(5):541-4
pubmed: 8562243
Blood. 2020 Jul 2;136(1):71-80
pubmed: 32244252
Clin Med (Lond). 2018 Apr 1;18(Suppl 2):s30-s35
pubmed: 29700090
Blood. 2017 Aug 3;130(5):597-605
pubmed: 28550039
Hematology Am Soc Hematol Educ Program. 2017 Dec 8;2017(1):1-12
pubmed: 29222231
Eur Heart J. 2018 Aug 7;39(30):2799-2806
pubmed: 29048471
Acta Haematol. 2020;143(4):343-351
pubmed: 32408301
P T. 2017 Jul;42(7):464-472
pubmed: 28674474
BMC Cardiovasc Disord. 2018 Dec 4;18(1):221
pubmed: 30509186
Circ Heart Fail. 2017 Jun;10(6):
pubmed: 28611125
Blood Rev. 2004 Mar;18(1):17-37
pubmed: 14684147
Herz. 2020 May;45(3):267-271
pubmed: 32107564
Circ Heart Fail. 2019 Sep;12(9):e006075
pubmed: 31480867
Clin Cardiol. 2021 Mar;44(3):322-331
pubmed: 33595871
Expert Rev Cardiovasc Ther. 2019 Sep;17(9):673-681
pubmed: 31478389
J Am Coll Cardiol. 2016 Sep 6;68(10):1014-20
pubmed: 27585505
J Am Coll Cardiol. 2015 Dec 1;66(21):2451-2466
pubmed: 26610878
J Am Coll Cardiol. 2017 Jul 25;70(4):466-477
pubmed: 28728692
ESC Heart Fail. 2019 Dec;6(6):1128-1139
pubmed: 31553132
Circulation. 2014 May 6;129(18):1840-9
pubmed: 24563469
Tex Heart Inst J. 2005;32(2):178-84
pubmed: 16107109
Rev Esp Cardiol (Engl Ed). 2017 Nov;70(11):991-1004
pubmed: 28870641
Blood. 2012 May 10;119(19):4391-4
pubmed: 22331188
Ann Noninvasive Electrocardiol. 2013 May;18(3):271-80
pubmed: 23714086
JAMA Cardiol. 2016 Nov 1;1(8):880-889
pubmed: 27557400
Curr Oncol Rep. 2017 Jul;19(7):46
pubmed: 28528458
J Am Coll Cardiol. 2016 Jul 12;68(2):161-72
pubmed: 27386769
Circulation. 2020 Jul 7;142(1):e7-e22
pubmed: 32476490
BMC Fam Pract. 2020 Sep 23;21(1):198
pubmed: 32967612
Heart. 2011 Jan;97(1):75-84
pubmed: 21148582
Curr Probl Cardiol. 2018 Jan;43(1):10-34
pubmed: 29173805
J Clin Oncol. 2012 Mar 20;30(9):989-95
pubmed: 22331953