What should we tell parents? Congenital diaphragmatic hernia.


Journal

Prenatal diagnosis
ISSN: 1097-0223
Titre abrégé: Prenat Diagn
Pays: England
ID NLM: 8106540

Informations de publication

Date de publication:
Mar 2022
Historique:
revised: 13 10 2020
received: 06 07 2020
accepted: 30 11 2020
pubmed: 19 2 2021
medline: 3 5 2022
entrez: 18 2 2021
Statut: ppublish

Résumé

Congenital diaphragmatic hernia (CDH) is characterized by a defect in the muscle dividing the thoracic and abdominal cavities. This leads to herniation of the abdominal organs into the thorax and a disturbance of lung development. Two-thirds of cases are identified by prenatal ultrasound in the second trimester, which should prompt referral to a tertiary center for prognosis assessment and counseling by a multidisciplinary team familiar with this condition. In this review, we summarize evidence on prenatal diagnosis and postnatal management of CDH. There is a focus on information that should be provided to expecting parents during prenatal counseling.

Identifiants

pubmed: 33599313
doi: 10.1002/pd.5880
doi:

Types de publication

Journal Article Review

Langues

eng

Sous-ensembles de citation

IM

Pagination

398-407

Subventions

Organisme : Great Ormond Street Hospital Charity
Organisme : CDH-UK/SPARKS

Informations de copyright

© 2020 John Wiley & Sons Ltd.

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Auteurs

Francesca M Russo (FM)

Clinical Department of Obstetrics and Gynaecology, University Hospitals Leuven, Leuven, Belgium.
Academic Department of Development and Regeneration, Cluster Woman and Child, KU Leuven, Leuven, Belgium.

Anne Debeer (A)

Academic Department of Development and Regeneration, Cluster Woman and Child, KU Leuven, Leuven, Belgium.
Neonatal Intensive Care Unit, University Hospitals Leuven, Leuven, Belgium.

Paolo De Coppi (P)

Neonatal and Paediatric Surgery Unit, Great Ormond Street Hospital, London, UK.
Stem Cells & Regenerative Medicine Section, NIHR Biomedical Research Center, UCL Great Ormond Street Institute of Child Health, London, UK.

Koenraad Devriendt (K)

Center for Human Genetics, University Hospitals Leuven, Leuven, Belgium.

Neeltje Crombag (N)

Academic Department of Development and Regeneration, Cluster Woman and Child, KU Leuven, Leuven, Belgium.

Talia Hubble (T)

Academic Department of Development and Regeneration, Cluster Woman and Child, KU Leuven, Leuven, Belgium.
Medical Sciences Division, University of Oxford, Oxford, UK.

Alexandra Benachi (A)

Department of Obstetrics and Gynecology, Hôpital Antoine Béclère, AP-HP, Université Paris Saclay, Clamart, France.
Centre Référence Maladie Rare: Hernie de Coupole Diaphragmatique, Clamart, France.

Jan Deprest (J)

Clinical Department of Obstetrics and Gynaecology, University Hospitals Leuven, Leuven, Belgium.
Academic Department of Development and Regeneration, Cluster Woman and Child, KU Leuven, Leuven, Belgium.
Institute for Women's Health, University College London, London, UK.

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