Sensitive protein misfolding cyclic amplification of sporadic Creutzfeldt-Jakob disease prions is strongly seed and substrate dependent.
Journal
Scientific reports
ISSN: 2045-2322
Titre abrégé: Sci Rep
Pays: England
ID NLM: 101563288
Informations de publication
Date de publication:
18 02 2021
18 02 2021
Historique:
received:
09
10
2020
accepted:
05
02
2021
entrez:
19
2
2021
pubmed:
20
2
2021
medline:
15
12
2021
Statut:
epublish
Résumé
Unlike variant Creutzfeldt-Jakob disease prions, sporadic Creutzfeldt-Jakob disease prions have been shown to be difficult to amplify in vitro by protein misfolding cyclic amplification (PMCA). We assessed PMCA of pathological prion protein (PrP
Identifiants
pubmed: 33603091
doi: 10.1038/s41598-021-83630-1
pii: 10.1038/s41598-021-83630-1
pmc: PMC7893054
doi:
Substances chimiques
Prion Proteins
0
Prions
0
Types de publication
Journal Article
Langues
eng
Sous-ensembles de citation
IM
Pagination
4058Subventions
Organisme : Agence Nationale de Sécurité du Médicament et des Produits de Santé
ID : PrionMDsecure
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