Giant Darier-Ferrand dermatofibrosarcoma protuberans of the abdomen and pelvis: a case report.
Darier–Ferrand dermatofibrosarcoma
Recurrent
Surgical resection
Journal
Journal of medical case reports
ISSN: 1752-1947
Titre abrégé: J Med Case Rep
Pays: England
ID NLM: 101293382
Informations de publication
Date de publication:
15 Mar 2021
15 Mar 2021
Historique:
received:
22
12
2020
accepted:
19
01
2021
entrez:
15
3
2021
pubmed:
16
3
2021
medline:
15
5
2021
Statut:
epublish
Résumé
Darier-Ferrand dermatofibrosarcoma (DFS) is a rare malignant cutaneous neoplasm characterized by local aggressiveness, high risk of recurrence, and low metastatic potential. A 60-year-old Tunisian man with recurrent abdominopelvic DFS for which he had undergone multiple excisions presented with an extensive DFS that invaded the external genitals. He underwent a large excision with emasculation and thin cutaneous graft of the abdominal wall and local skin flap in the pelvis. DFS is a rare yet recurrent skin tumor. Wide excision with free margins remains the cornerstone of treatment. We report a case of a giant DFS treated with wide excision and reconstructive surgery to cover the defect.
Sections du résumé
BACKGROUND
BACKGROUND
Darier-Ferrand dermatofibrosarcoma (DFS) is a rare malignant cutaneous neoplasm characterized by local aggressiveness, high risk of recurrence, and low metastatic potential.
CASE PRESENTATION
METHODS
A 60-year-old Tunisian man with recurrent abdominopelvic DFS for which he had undergone multiple excisions presented with an extensive DFS that invaded the external genitals. He underwent a large excision with emasculation and thin cutaneous graft of the abdominal wall and local skin flap in the pelvis.
CONCLUSION
CONCLUSIONS
DFS is a rare yet recurrent skin tumor. Wide excision with free margins remains the cornerstone of treatment. We report a case of a giant DFS treated with wide excision and reconstructive surgery to cover the defect.
Identifiants
pubmed: 33715634
doi: 10.1186/s13256-021-02687-8
pii: 10.1186/s13256-021-02687-8
pmc: PMC7958428
doi:
Types de publication
Case Reports
Journal Article
Langues
eng
Sous-ensembles de citation
IM
Pagination
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