Insights from Cardiopulmonary Exercise Testing in Pediatric Patients with Hypertrophic Cardiomyopathy.


Journal

Biomolecules
ISSN: 2218-273X
Titre abrégé: Biomolecules
Pays: Switzerland
ID NLM: 101596414

Informations de publication

Date de publication:
02 03 2021
Historique:
received: 12 01 2021
revised: 22 02 2021
accepted: 24 02 2021
entrez: 3 4 2021
pubmed: 4 4 2021
medline: 16 9 2021
Statut: epublish

Résumé

The usefulness of cardiopulmonary exercise test (CPET) in adult hypertrophic cardiomyopathy (HCM) patients is well-known, whereas its role in pediatric HCM patients has not yet been explored. The present study investigates possible insights from a CPET assessment in a cohort of pediatric HCM outpatients in terms of functional and prognostic assessment. Sixty consecutive pediatric HCM outpatients aged <18 years old were enrolled, each of them undergoing a full clinical assessment including a CPET; a group of 60 healthy subjects served as controls. A unique composite end-point of heart failure (HF) related and sudden cardiac death (SCD) or SCD-equivalent events was also explored. During a median follow-up of 53 months (25th-75th: 13-84 months), a total of 13 HF- and 7 SCD-related first events were collected. Compared to controls, HCM patients showed an impaired functional capacity with most of them showing peak oxygen uptake (pVO

Identifiants

pubmed: 33801562
pii: biom11030376
doi: 10.3390/biom11030376
pmc: PMC7999553
pii:
doi:

Types de publication

Journal Article Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Subventions

Organisme : Sapienza Università di Roma
ID : RM11916B4B1FA2A6

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Auteurs

Giovanna Gallo (G)

Department of Clinical and Molecular Medicine, Sapienza University, 00189 Rome, Italy.

Vittoria Mastromarino (V)

Paediatric Cardiology and ACHD Unit, S. Orsola, Malpighi Hospital, 40138 Bologna, Italy.

Giuseppe Limongelli (G)

Cardiologia SUN, Monaldi Hospital, II University of Naples, 80100 Naples, Italy.

Giulio Calcagni (G)

Department of Pediatric Cardiology and Cardiac Surgery, Bambino Gesù Children's Hospital, IRCCS, 00050 Rome, Italy.

Antonello Maruotti (A)

Department of Scienze Economiche, Politiche e delle Lingue Moderne, Libera Università SS Maria Assunta, 00193 Rome, Italy.
Department of Mathematics, University of Bergen, 5052 Bergen, Norway.
School of Computing, University of Portsmouth, Portsmouth PO2 8QD, UK.

Luca Ragni (L)

Paediatric Cardiology and ACHD Unit, S. Orsola, Malpighi Hospital, 40138 Bologna, Italy.

Fabio Valente (F)

Cardiologia SUN, Monaldi Hospital, II University of Naples, 80100 Naples, Italy.

Maria Beatrice Musumeci (MB)

Department of Clinical and Molecular Medicine, Sapienza University, 00189 Rome, Italy.

Rachele Adorisio (R)

Department of Pediatric Cardiology and Cardiac Surgery, Bambino Gesù Children's Hospital, IRCCS, 00050 Rome, Italy.

Marta Rubino (M)

Cardiologia SUN, Monaldi Hospital, II University of Naples, 80100 Naples, Italy.

Camillo Autore (C)

Department of Clinical and Molecular Medicine, Sapienza University, 00189 Rome, Italy.

Damiano Magrì (D)

Department of Clinical and Molecular Medicine, Sapienza University, 00189 Rome, Italy.

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