Central human B cell tolerance manifests with a distinctive cell phenotype and is enforced via CXCR4 signaling in hu-mice.


Journal

Proceedings of the National Academy of Sciences of the United States of America
ISSN: 1091-6490
Titre abrégé: Proc Natl Acad Sci U S A
Pays: United States
ID NLM: 7505876

Informations de publication

Date de publication:
20 04 2021
Historique:
entrez: 14 4 2021
pubmed: 15 4 2021
medline: 15 12 2021
Statut: ppublish

Résumé

Central B cell tolerance, the process restricting the development of many newly generated autoreactive B cells, has been intensely investigated in mouse cells while studies in humans have been hampered by the inability to phenotypically distinguish autoreactive and nonautoreactive immature B cell clones and the difficulty in accessing fresh human bone marrow samples. Using a human immune system mouse model in which all human Igκ

Identifiants

pubmed: 33850015
pii: 2021570118
doi: 10.1073/pnas.2021570118
pmc: PMC8072395
pii:
doi:

Substances chimiques

Autoantibodies 0
Autoantigens 0
CXCR4 protein, human 0
Receptors, Antigen, B-Cell 0
Receptors, CXCR4 0

Types de publication

Journal Article Research Support, N.I.H., Extramural

Langues

eng

Sous-ensembles de citation

IM

Subventions

Organisme : NIAID NIH HHS
ID : R21 AI131639
Pays : United States
Organisme : NIAID NIH HHS
ID : R01 AI136534
Pays : United States
Organisme : NCATS NIH HHS
ID : UL1 TR002535
Pays : United States
Organisme : NIAID NIH HHS
ID : R21 AI063321
Pays : United States
Organisme : NIAID NIH HHS
ID : R01 AI124474
Pays : United States
Organisme : NIAID NIH HHS
ID : R01 AI152535
Pays : United States

Déclaration de conflit d'intérêts

The authors declare no competing interest.

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Auteurs

Thiago Alves da Costa (T)

Department of Immunology and Microbiology, University of Colorado Anschutz Medical Campus, Aurora, CO 80045.

Jacob N Peterson (JN)

Department of Immunology and Microbiology, University of Colorado Anschutz Medical Campus, Aurora, CO 80045.

Julie Lang (J)

Department of Immunology and Microbiology, University of Colorado Anschutz Medical Campus, Aurora, CO 80045.

Jeremy Shulman (J)

Department of Immunology and Microbiology, University of Colorado Anschutz Medical Campus, Aurora, CO 80045.

Xiayuan Liang (X)

Department of Pathology, University of Colorado School of Medicine and Children's Hospital of Colorado, Aurora, CO 80045.

Brian M Freed (BM)

Department of Medicine, Division of Allergy and Clinical Immunology, University of Colorado Anschutz Medical Campus, Aurora, CO 80045.

Susan A Boackle (SA)

Department of Medicine, Division of Rheumatology, University of Colorado Anschutz Medical Campus, Aurora, CO 80045.

Pilar Lauzurica (P)

Department of Immunology, Centro Nacional de Microbiologia, Majadahonda, 28222 Madrid, Spain.

Raul M Torres (RM)

Department of Immunology and Microbiology, University of Colorado Anschutz Medical Campus, Aurora, CO 80045.
Department of Immunology and Genomic Medicine, National Jewish Health, Denver, CO 80206.

Roberta Pelanda (R)

Department of Immunology and Microbiology, University of Colorado Anschutz Medical Campus, Aurora, CO 80045; roberta.pelanda@cuanschutz.edu.
Department of Immunology and Genomic Medicine, National Jewish Health, Denver, CO 80206.

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Classifications MeSH