Pancreatic Neuroendocrine Neoplasms in Multiple Endocrine Neoplasia Type 1.
MEN1 gene
Multiple Endocrine Neoplasia type 1 (MEN1)
epigenetic factors
gene mutation
menin
pancreatic neuroendocrine tumors (pNETs)
Journal
International journal of molecular sciences
ISSN: 1422-0067
Titre abrégé: Int J Mol Sci
Pays: Switzerland
ID NLM: 101092791
Informations de publication
Date de publication:
14 Apr 2021
14 Apr 2021
Historique:
received:
31
03
2021
revised:
12
04
2021
accepted:
12
04
2021
entrez:
30
4
2021
pubmed:
1
5
2021
medline:
14
5
2021
Statut:
epublish
Résumé
Pancreatic neuroendocrine tumors (pNETs) are a rare group of cancers accounting for about 1-2% of all pancreatic neoplasms. About 10% of pNETs arise within endocrine tumor syndromes, such as Multiple Endocrine Neoplasia type 1 (MEN1). pNETs affect 30-80% of MEN1 patients, manifesting prevalently as multiple microadenomas. pNETs in patients with MEN1 are particularly difficult to treat due to differences in their growth potential, their multiplicity, the frequent requirement of extensive surgery, the high rate of post-operative recurrences, and the concomitant development of other tumors. MEN1 syndrome is caused by germinal heterozygote inactivating mutation of the
Identifiants
pubmed: 33919851
pii: ijms22084041
doi: 10.3390/ijms22084041
pmc: PMC8070788
pii:
doi:
Types de publication
Journal Article
Review
Langues
eng
Sous-ensembles de citation
IM
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