NanoString technology distinguishes anti-TIF-1γ
Mi-2
NanoString
TIF-1γ
dermatomyositis
myositis-specific antibody
skeletal muscle
Journal
Brain pathology (Zurich, Switzerland)
ISSN: 1750-3639
Titre abrégé: Brain Pathol
Pays: Switzerland
ID NLM: 9216781
Informations de publication
Date de publication:
05 2021
05 2021
Historique:
revised:
22
03
2021
received:
11
02
2021
accepted:
23
03
2021
entrez:
27
5
2021
pubmed:
28
5
2021
medline:
3
2
2022
Statut:
ppublish
Résumé
Dermatomyositis (DM) is a systemic idiopathic inflammatory disease affecting skeletal muscle and skin, clinically characterized by symmetrical proximal muscle weakness and typical skin lesions. Recently, myositis-specific autoantibodies (MSA) became of utmost importance because they strongly correlate with distinct clinical manifestations and prognosis. Antibodies against transcription intermediary factor 1γ (TIF-1γ) are frequently associated with increased risk of malignancy, a specific cutaneous phenotype and limited response to therapy in adult DM patients. Anti-Mi-2 autoantibodies, in contrast, are typically associated with classic DM rashes, prominent skeletal muscle weakness, better therapeutic response and prognosis, and less frequently with cancer. Nevertheless, the sensitivity of autoantibody testing is only moderate, and alternative reliable methods for DM patient stratification and prediction of cancer risk are needed. To further investigate these clinically distinct DM subgroups, we herein analyzed 30 DM patients (n = 15 Mi-2
Identifiants
pubmed: 34043263
doi: 10.1111/bpa.12957
pmc: PMC8412076
doi:
Substances chimiques
Autoantibodies
0
Mi-2 antibodies
0
Signaling Lymphocytic Activation Molecule Family
0
Transcription Factors
0
Types de publication
Journal Article
Research Support, Non-U.S. Gov't
Langues
eng
Sous-ensembles de citation
IM
Pagination
e12957Commentaires et corrections
Type : ErratumIn
Informations de copyright
© 2021 The Authors. Brain Pathology published by John Wiley & Sons Ltd on behalf of International Society of Neuropathology.
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