Treatment with a GSK-3β/HDAC Dual Inhibitor Restores Neuronal Survival and Maturation in an In Vitro and In Vivo Model of
Animals
Cell Line
Cell Survival
/ drug effects
Epileptic Syndromes
/ drug therapy
Glycogen Synthase Kinase 3 beta
/ antagonists & inhibitors
Hippocampus
/ drug effects
Histone Deacetylase Inhibitors
/ pharmacology
Humans
Mice
Mice, Inbred C57BL
Mice, Knockout
Neurons
/ drug effects
Spasms, Infantile
/ drug therapy
CDKL5 deficiency disorder
GSK-3β
HDAC6
dual inhibitor
hippocampal defects
neuronal survival
synapse development
Journal
International journal of molecular sciences
ISSN: 1422-0067
Titre abrégé: Int J Mol Sci
Pays: Switzerland
ID NLM: 101092791
Informations de publication
Date de publication:
31 May 2021
31 May 2021
Historique:
received:
22
04
2021
revised:
26
05
2021
accepted:
28
05
2021
entrez:
2
6
2021
pubmed:
3
6
2021
medline:
22
7
2021
Statut:
epublish
Résumé
Mutations in the X-linked cyclin-dependent kinase-like 5 (
Identifiants
pubmed: 34073043
pii: ijms22115950
doi: 10.3390/ijms22115950
pmc: PMC8198396
pii:
doi:
Substances chimiques
Histone Deacetylase Inhibitors
0
Glycogen Synthase Kinase 3 beta
EC 2.7.11.1
Types de publication
Journal Article
Langues
eng
Sous-ensembles de citation
IM
Subventions
Organisme : Fondazione Telethon
ID : GGP19045
Organisme : Italian association:CDKL5 insieme verso la cura
ID : Ciani
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