Sarcoidosis-Related Cardiomyopathy: Current Knowledge, Challenges, and Future Perspectives State-of-the-Art Review.
cardiac sarcoidosis
heart transplantation
inflammatory cardiomyopathy
interdisciplinary
myocarditis
Journal
Journal of cardiac failure
ISSN: 1532-8414
Titre abrégé: J Card Fail
Pays: United States
ID NLM: 9442138
Informations de publication
Date de publication:
01 2022
01 2022
Historique:
received:
16
05
2021
accepted:
21
06
2021
pubmed:
15
7
2021
medline:
1
3
2022
entrez:
14
7
2021
Statut:
ppublish
Résumé
The prevalence of sarcoidosis-related cardiomyopathy is increasing. Sarcoidosis impacts cardiac function through granulomatous infiltration of the heart, resulting in conduction disease, arrhythmia, and/or heart failure. The diagnosis of cardiac sarcoidosis (CS) can be challenging and requires clinician awareness as well as differentiation from overlapping diagnostic phenotypes, such as other forms of myocarditis and arrhythmogenic cardiomyopathy. Clinical manifestations, extracardiac involvement, histopathology, and advanced cardiac imaging can all lend support to a diagnosis of CS. The mainstay of therapy for CS is immunosuppression; however, no prospective clinical trials exist to guide management. Patients may progress to developing advanced heart failure or ventricular arrhythmia, for which ventricular assist device therapies or heart transplantation may be considered. The existing knowledge gaps in CS call for an interdisciplinary approach to both patient care and future investigation to improve mechanistic understanding and therapeutic strategies.
Identifiants
pubmed: 34260889
pii: S1071-9164(21)00264-5
doi: 10.1016/j.cardfail.2021.06.016
pmc: PMC8748280
mid: NIHMS1728681
pii:
doi:
Types de publication
Journal Article
Review
Langues
eng
Sous-ensembles de citation
IM
Pagination
113-132Subventions
Organisme : NHLBI NIH HHS
ID : K23 HL148527
Pays : United States
Organisme : NINR NIH HHS
ID : T32 NR012704
Pays : United States
Informations de copyright
Copyright © 2021 Elsevier Inc. All rights reserved.
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