The Cellular Prion Protein Increases the Uptake and Toxicity of TDP-43 Fibrils.
PrPC
TDP-43
fibrils
toxicity
uptake
Journal
Viruses
ISSN: 1999-4915
Titre abrégé: Viruses
Pays: Switzerland
ID NLM: 101509722
Informations de publication
Date de publication:
17 08 2021
17 08 2021
Historique:
received:
20
07
2021
revised:
11
08
2021
accepted:
14
08
2021
entrez:
28
8
2021
pubmed:
29
8
2021
medline:
28
1
2022
Statut:
epublish
Résumé
Cytoplasmic aggregation of the primarily nuclear TAR DNA-binding protein 43 (TDP-43) affects neurons in most amyotrophic lateral sclerosis (ALS) and approximately half of frontotemporal lobar degeneration (FTLD) cases. The cellular prion protein, PrP
Identifiants
pubmed: 34452489
pii: v13081625
doi: 10.3390/v13081625
pmc: PMC8402629
pii:
doi:
Substances chimiques
DNA-Binding Proteins
0
PrPC Proteins
0
Prion Proteins
0
Prnp protein, mouse
0
TARDBP protein, human
0
TDP-43 protein, mouse
0
Types de publication
Journal Article
Research Support, Non-U.S. Gov't
Langues
eng
Sous-ensembles de citation
IM
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