A reanalysis of pain crises data from the pivotal l-glutamine in sickle cell disease trial.

Annual crisis rate Endari Pain crises Sickle cell disease l-glutamine

Journal

Contemporary clinical trials
ISSN: 1559-2030
Titre abrégé: Contemp Clin Trials
Pays: United States
ID NLM: 101242342

Informations de publication

Date de publication:
11 2021
Historique:
received: 10 05 2021
revised: 23 08 2021
accepted: 24 08 2021
pubmed: 13 9 2021
medline: 25 11 2021
entrez: 12 9 2021
Statut: ppublish

Résumé

The pivotal Endari trial in sickle cell disease showed a reduction in pain crises events. This reanalysis of the l-glutamine phase 3 trial using annual rates of pain crises, consistent with other SCD studies, supported the statistically significant outcomes of the original analysis. The observed 45% difference in the VOC rate is comparable to what was reported in other sickle cell therapeutics used to reduce the incidence of pain. The results presented in this communication are informative for clinicians evaluating treatment effects across available SCD therapeutic options based on studies that utilized VOC as the primary endpoint.

Identifiants

pubmed: 34509600
pii: S1551-7144(21)00282-2
doi: 10.1016/j.cct.2021.106546
pii:
doi:

Substances chimiques

Glutamine 0RH81L854J

Types de publication

Journal Article Research Support, Non-U.S. Gov't

Langues

eng

Sous-ensembles de citation

IM

Pagination

106546

Informations de copyright

Copyright © 2021 The Authors. Published by Elsevier Inc. All rights reserved.

Auteurs

Ahmar U Zaidi (AU)

Children's Hospital of Michigan, Central Michigan University, 3901 Beaubien, Detroit, 48201 Detroit, MI, United States of America. Electronic address: zaidi1au@cmich.edu.

Jeremie Estepp (J)

St. Jude Children's Research Hospital, Memphis, TN, United States of America.

Nirmish Shah (N)

Duke University School of Medicine, Durham, NC, United States of America.

Salam Alkindi (S)

College of Medicine and Health Sciences, Sultan Qaboos University, Muscat, Oman.

Hatoon Ezzat (H)

St. Paul's Hospital, University of British Columbia, Vancouver, BC, Canada.

Hung Lam (H)

MMS, Canton, MI, United States of America.

Caterina P Minniti (CP)

Einstein College of Medicine, Montefiore Hospital, Bronx, NY, United States of America.

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Classifications MeSH