Trends in diagnosis, referral, red flag onset, patient profiles and natural outcome of de novo cardiac amyloidosis and their multidisciplinary implications.
ATTR amyloidosis
cardiac amyloidosis
outcome
red flags
transthyretin
Journal
Acta cardiologica
ISSN: 1784-973X
Titre abrégé: Acta Cardiol
Pays: England
ID NLM: 0370570
Informations de publication
Date de publication:
Nov 2022
Nov 2022
Historique:
pubmed:
28
9
2021
medline:
13
1
2023
entrez:
27
9
2021
Statut:
ppublish
Résumé
Cardiac amyloidosis (CA) is often overlooked or misdiagnosed. Effects of growing disease awareness, diagnostic ameliorations and novel treatment options on CA diagnosis and management are scarcely reported. To report trends in diagnosis, referral routes, clinical presentation, early onset diagnostic red flags and outcome in de novo CA subjects. An unselected cohort of 139 de novo CA patients over an 8-year period in a tertiary referral hospital was recruited. Transthyretin (ATTR, 82%, Although CA diagnostic uptake and referral improve, specialist-specific disease and diagnostic red flag ignorance result in non-timely diagnosis and unfavourable outcome.
Sections du résumé
BACKGROUND
UNASSIGNED
Cardiac amyloidosis (CA) is often overlooked or misdiagnosed. Effects of growing disease awareness, diagnostic ameliorations and novel treatment options on CA diagnosis and management are scarcely reported.
OBJECTIVE
UNASSIGNED
To report trends in diagnosis, referral routes, clinical presentation, early onset diagnostic red flags and outcome in de novo CA subjects.
METHODS
UNASSIGNED
An unselected cohort of 139 de novo CA patients over an 8-year period in a tertiary referral hospital was recruited.
RESULTS
UNASSIGNED
Transthyretin (ATTR, 82%,
CONCLUSIONS
UNASSIGNED
Although CA diagnostic uptake and referral improve, specialist-specific disease and diagnostic red flag ignorance result in non-timely diagnosis and unfavourable outcome.
Identifiants
pubmed: 34565298
doi: 10.1080/00015385.2021.1976450
doi:
Types de publication
Journal Article
Langues
eng
Sous-ensembles de citation
IM