Hemopericardium with cardiac tamponade as a rare presentation of a massive aortic aneurysm in a young child with autosomal recessive cutis laxa.
aortic aneurysm
cutis laxa
hemopericardium
tamponade
Journal
Echocardiography (Mount Kisco, N.Y.)
ISSN: 1540-8175
Titre abrégé: Echocardiography
Pays: United States
ID NLM: 8511187
Informations de publication
Date de publication:
12 2021
12 2021
Historique:
revised:
01
11
2021
received:
02
09
2021
accepted:
08
11
2021
pubmed:
1
12
2021
medline:
27
1
2022
entrez:
30
11
2021
Statut:
ppublish
Résumé
Aortic aneurysms are rare in the pediatric age group and are commonly caused by genetic disorders associated with vasculopathy, weakness and fragility of arterial walls with progressive dilatation or even rupture. We reported a giant aortic aneurysm involving the ascending aorta and aortic arch in a 20-month-old girl with autosomal recessive cutis laxa type 1B (ARCL1B) who presented with hemorrhagic pericardial effusion and tamponade (impending rupture). Successful surgical repair has been done through excision of the aneurysmal part and replacement by Hemashield graft with preservation of the aortic valve.
Types de publication
Case Reports
Langues
eng
Sous-ensembles de citation
IM
Pagination
2095-2099Informations de copyright
© 2021 Wiley Periodicals LLC.
Références
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