Case Report: Evolution of a Severe Vascular Refractory Form of ECD Requiring Liver Transplantation Correlated With the Change in the Monocyte Subset Analysis.


Journal

Frontiers in immunology
ISSN: 1664-3224
Titre abrégé: Front Immunol
Pays: Switzerland
ID NLM: 101560960

Informations de publication

Date de publication:
2021
Historique:
received: 09 08 2021
accepted: 21 10 2021
entrez: 6 12 2021
pubmed: 7 12 2021
medline: 8 2 2022
Statut: epublish

Résumé

Erdheim-Chester disease is a rare histiocytosis characterized by iconic features associated with compatible histology. Most patients have somatic mutations in the MAP-kinase pathway gene, and the mutations occur in CD14

Identifiants

pubmed: 34867991
doi: 10.3389/fimmu.2021.755846
pmc: PMC8633538
doi:

Types de publication

Case Reports

Langues

eng

Sous-ensembles de citation

IM

Pagination

755846

Informations de copyright

Copyright © 2021 Razanamahery, Roggy, Emile, Malakhia, Lakkis, Garnache-Ottou, Soumagne, Cohen-Aubart, Haroche and Bonnotte.

Déclaration de conflit d'intérêts

The authors declare that the research was conducted in the absence of any commercial or financial relationships that could be construed as a potential conflict of interest.

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Auteurs

Jérôme Razanamahery (J)

Department of Internal Medicine and Clinical Immunology, Francois Mitterrand Hospital, Dijon University Hospital, Dijon, France.

Anne Roggy (A)

Établissement Français du Sang Bourgogne Franche-Comté, Laboratoire d'Hématologie et d'Immunologie Régional, Besançon, France.

Jean-François Emile (JF)

Department of Pathology, Ambroise-Paré Hospital, Assistance-Publique Hopitaux de Paris, Paris, France.

Alexandre Malakhia (A)

Department of Radiology, Francois Mitterrand Hospital, Dijon University Hospital, Dijon, France.

Zaher Lakkis (Z)

Digestive Surgery Unit, University of Bourgogne Franche-Comté, Centre Hospitalier Regional Universitaire (CHRU) Besançon, Besancon, France.

Francine Garnache-Ottou (F)

Établissement Français du Sang Bourgogne Franche-Comté, Laboratoire d'Hématologie et d'Immunologie Régional, Besançon, France.

Thibaud Soumagne (T)

Department of Intensive Care Unit, Besancon University Hospital, Besancon, France.

Fleur Cohen-Aubart (F)

Internal Medicine Department 2, National Reference Center for Histiocytosis, Pitié-Salpêtrière Hospital, Assistance Publique Hôpitaux de Paris, Paris, France.

Julien Haroche (J)

Internal Medicine Department 2, National Reference Center for Histiocytosis, Pitié-Salpêtrière Hospital, Assistance Publique Hôpitaux de Paris, Paris, France.

Bernard Bonnotte (B)

Department of Internal Medicine and Clinical Immunology, Francois Mitterrand Hospital, Dijon University Hospital, Dijon, France.

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